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109991003: Acute panmyelosis with myelofibrosis (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 01-May 2024. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
344846014 Acute myelofibrosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
2532080014 Acute panmyelosis with myelofibrosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5348998013 Acute myelosclerosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5349008010 Acute panmyelosis with myelofibrosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
5348999017 A rare unclassified acute myeloid leukemia characterized by an acute panmyeloid proliferation with blasts constituting more than 20% of cells in the bone marrow or peripheral blood, accompanied by fibrosis of the bone marrow. Patients typically present with acute onset of severe constitutional symptoms, bone pain, and pancytopenia. Splenomegaly is minimal or absent. The disease is rapidly progressive with poor therapy response. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5349000015 A rare unclassified acute myeloid leukaemia characterised by an acute panmyeloid proliferation with blasts constituting more than 20% of cells in the bone marrow or peripheral blood, accompanied by fibrosis of the bone marrow. Patients typically present with acute onset of severe constitutional symptoms, bone pain, and pancytopenia. Splenomegaly is minimal or absent. The disease is rapidly progressive with poor therapy response. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
174692019 Acute myelofibrosis (clinical) en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
174692019 Acute myelofibrosis (clinical) en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
344846014 Acute myelofibrosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
344846014 Acute myelofibrosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
617862013 Acute myelofibrosis (disorder) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
617862013 Acute myelofibrosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
2532080014 Acute panmyelosis with myelofibrosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
2532080014 Acute panmyelosis with myelofibrosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5348998013 Acute myelosclerosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5349008010 Acute panmyelosis with myelofibrosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
5348999017 A rare unclassified acute myeloid leukemia characterized by an acute panmyeloid proliferation with blasts constituting more than 20% of cells in the bone marrow or peripheral blood, accompanied by fibrosis of the bone marrow. Patients typically present with acute onset of severe constitutional symptoms, bone pain, and pancytopenia. Splenomegaly is minimal or absent. The disease is rapidly progressive with poor therapy response. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5349000015 A rare unclassified acute myeloid leukaemia characterised by an acute panmyeloid proliferation with blasts constituting more than 20% of cells in the bone marrow or peripheral blood, accompanied by fibrosis of the bone marrow. Patients typically present with acute onset of severe constitutional symptoms, bone pain, and pancytopenia. Splenomegaly is minimal or absent. The disease is rapidly progressive with poor therapy response. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3414901001000117 Akute Panmyelose mit Myelofibrose de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
4746811000241112 panmyélose aigüe avec myélofibrose fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
4746811000241112 panmyélose aigüe avec myélofibrose fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3414901001000117 Akute Panmyelose mit Myelofibrose de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Acute panmyelosis with myelofibrosis (disorder) Is a néoplasme selon la localisation corporelle false Inferred relationship Existential restriction modifier (core metadata concept)
Acute panmyelosis with myelofibrosis (disorder) Is a Acute myeloid leukemia, disease true Inferred relationship Existential restriction modifier (core metadata concept)
Acute panmyelosis with myelofibrosis (disorder) Is a Myelofibrosis true Inferred relationship Existential restriction modifier (core metadata concept)
Acute panmyelosis with myelofibrosis (disorder) Associated morphology [M]Acute myelofibrosis false Inferred relationship Existential restriction modifier (core metadata concept) 2
Acute panmyelosis with myelofibrosis (disorder) Pathological process Neoplastic process false Inferred relationship Existential restriction modifier (core metadata concept)
Acute panmyelosis with myelofibrosis (disorder) Associated morphology Myeloid leukemia - category false Inferred relationship Existential restriction modifier (core metadata concept) 4
Acute panmyelosis with myelofibrosis (disorder) Associated morphology néoplasie maligne (morphologie) false Inferred relationship Existential restriction modifier (core metadata concept) 5
Acute panmyelosis with myelofibrosis (disorder) Finding site Lymphoid system structure false Inferred relationship Existential restriction modifier (core metadata concept) 2
Acute panmyelosis with myelofibrosis (disorder) Associated morphology Acute leukemia (morphologic abnormality) false Inferred relationship Existential restriction modifier (core metadata concept) 2
Acute panmyelosis with myelofibrosis (disorder) Associated morphology Reticulin fibrosis true Inferred relationship Existential restriction modifier (core metadata concept) 2
Acute panmyelosis with myelofibrosis (disorder) Pathological process Malignant neoplastic process false Inferred relationship Existential restriction modifier (core metadata concept) 1
Acute panmyelosis with myelofibrosis (disorder) Course Acute false Inferred relationship Existential restriction modifier (core metadata concept)
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 4
Acute panmyelosis with myelofibrosis (disorder) Associated morphology Acute myeloid leukemia, no International Classification of Diseases for Oncology subtype false Inferred relationship Existential restriction modifier (core metadata concept) 1
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 1
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 1
Acute panmyelosis with myelofibrosis (disorder) Finding site Hematopoietic system structure false Inferred relationship Existential restriction modifier (core metadata concept) 5
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 2
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 4
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 1
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 3
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 3
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 1
Acute panmyelosis with myelofibrosis (disorder) Associated morphology Reticulin fibrosis false Inferred relationship Existential restriction modifier (core metadata concept) 3
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 3
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 4
Acute panmyelosis with myelofibrosis (disorder) Finding site Hematopoietic system structure false Inferred relationship Existential restriction modifier (core metadata concept) 2
Acute panmyelosis with myelofibrosis (disorder) Associated morphology néoplasie maligne (morphologie) false Inferred relationship Existential restriction modifier (core metadata concept) 2
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 1
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 2
Acute panmyelosis with myelofibrosis (disorder) Associated morphology Acute panmyelosis with myelofibrosis false Inferred relationship Existential restriction modifier (core metadata concept) 1
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 1
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 2
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 1
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 2
Acute panmyelosis with myelofibrosis (disorder) Is a Neoplasm of bone marrow false Inferred relationship Existential restriction modifier (core metadata concept)
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone structure false Inferred relationship Existential restriction modifier (core metadata concept)
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure false Inferred relationship Existential restriction modifier (core metadata concept) 1
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure true Inferred relationship Existential restriction modifier (core metadata concept) 2
Acute panmyelosis with myelofibrosis (disorder) Finding site Bone marrow structure true Inferred relationship Existential restriction modifier (core metadata concept) 1
Acute panmyelosis with myelofibrosis (disorder) Associated morphology Acute panmyelosis with myelofibrosis false Inferred relationship Existential restriction modifier (core metadata concept) 1
Acute panmyelosis with myelofibrosis (disorder) Associated morphology Acute myeloid leukaemia true Inferred relationship Existential restriction modifier (core metadata concept) 1

Inbound Relationships Type Active Source Characteristic Refinability Group
Acute myelofibrosis in remission Is a False Acute panmyelosis with myelofibrosis (disorder) Inferred relationship Existential restriction modifier (core metadata concept)

Reference Sets

Component annotation with string value reference set (foundation metadata concept)

Concept inactivation indicator attribute value reference set (foundation metadata concept)

SAME AS association reference set (foundation metadata concept)

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