1172606002: Idiopathic pleuroparenchymal fibroelastosis (disorder)

SNOMED CT Concept\Clinical finding (finding)\...

\Viscus structure finding (finding)\Lung finding\Disease of lung (disorder)\...

\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)

\Lung consolidation\Idiopathic pleuroparenchymal fibroelastosis (disorder)

\Finding of trunk structure\Finding of upper trunk (finding)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disorder of soft tissue of thoracic cavity\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Finding of upper trunk (finding)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disorder of soft tissue of thoracic cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Finding of upper trunk (finding)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disorder of pleura and pleural cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Finding of upper trunk (finding)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disease of lung (disorder)\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Finding of upper trunk (finding)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disease of lung (disorder)\Lung consolidation\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Finding of upper trunk (finding)\Finding of region of thorax\Pleura finding\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Finding of upper trunk (finding)\Finding of region of thorax\Lung finding\Disease of lung (disorder)\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Finding of upper trunk (finding)\Finding of region of thorax\Lung finding\Disease of lung (disorder)\Lung consolidation\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Finding of upper trunk (finding)\Finding of region of thorax\Disorder of thorax (disorder)\Disorder of soft tissue of thoracic cavity\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Finding of upper trunk (finding)\Finding of region of thorax\Disorder of thorax (disorder)\Disorder of soft tissue of thoracic cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Finding of upper trunk (finding)\Finding of region of thorax\Disorder of thorax (disorder)\Disorder of pleura and pleural cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Finding of upper trunk (finding)\Finding of region of thorax\Disorder of thorax (disorder)\Disease of lung (disorder)\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Finding of upper trunk (finding)\Finding of region of thorax\Disorder of thorax (disorder)\Disease of lung (disorder)\Lung consolidation\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disorder of soft tissue of thoracic cavity\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disorder of soft tissue of thoracic cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disorder of pleura and pleural cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disease of lung (disorder)\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disease of lung (disorder)\Lung consolidation\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disorder of soft tissue of trunk\Disorder of soft tissue of thoracic cavity\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disorder of soft tissue of trunk\Disorder of soft tissue of thoracic cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disorder of soft tissue of body cavity\Disorder of soft tissue of thoracic cavity\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Finding of trunk structure\Disorder of trunk (disorder)\Disorder of soft tissue of body cavity\Disorder of soft tissue of thoracic cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)

\General finding of soft tissue\Pleura finding\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\General finding of soft tissue\Disorder of soft tissue\Disorder of soft tissue of trunk\Disorder of soft tissue of thoracic cavity\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\General finding of soft tissue\Disorder of soft tissue\Disorder of soft tissue of trunk\Disorder of soft tissue of thoracic cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\General finding of soft tissue\Disorder of soft tissue\Disorder of soft tissue of body cavity\Disorder of soft tissue of thoracic cavity\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\General finding of soft tissue\Disorder of soft tissue\Disorder of soft tissue of body cavity\Disorder of soft tissue of thoracic cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\General finding of soft tissue\Disorder of soft tissue\Lesion of soft tissue (disorder)\Idiopathic pleuroparenchymal fibroelastosis (disorder)

\Respiratory finding\Pleura finding\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Respiratory finding\Lower respiratory tract finding\Lung finding\Disease of lung (disorder)\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Respiratory finding\Lower respiratory tract finding\Lung finding\Disease of lung (disorder)\Lung consolidation\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Respiratory finding\Lower respiratory tract finding\Inflammatory disorder of lower respiratory tract\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Respiratory finding\Disorder of respiratory system\Inflammatory disorder of the respiratory system (disorder)\Inflammatory disorder of the respiratory tract\Inflammatory disorder of lower respiratory tract\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Respiratory finding\Disorder of respiratory system\Disease of lower respiratory system\Disorder of pleura and pleural cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Respiratory finding\Disorder of respiratory system\Disease of lower respiratory system\Inflammatory disorder of lower respiratory tract\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Respiratory finding\Disorder of respiratory system\Disease of lower respiratory system\Disease of lung (disorder)\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Respiratory finding\Disorder of respiratory system\Disease of lower respiratory system\Disease of lung (disorder)\Lung consolidation\Idiopathic pleuroparenchymal fibroelastosis (disorder)

\Disease\Degenerative disorder\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of body system\Inflammation of specific body systems\Inflammatory disorder of the respiratory system (disorder)\Inflammatory disorder of the respiratory tract\Inflammatory disorder of lower respiratory tract\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of body system\Disorder of respiratory system\Inflammatory disorder of the respiratory system (disorder)\Inflammatory disorder of the respiratory tract\Inflammatory disorder of lower respiratory tract\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of body system\Disorder of respiratory system\Disease of lower respiratory system\Disorder of pleura and pleural cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of body system\Disorder of respiratory system\Disease of lower respiratory system\Inflammatory disorder of lower respiratory tract\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of body system\Disorder of respiratory system\Disease of lower respiratory system\Disease of lung (disorder)\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of body system\Disorder of respiratory system\Disease of lower respiratory system\Disease of lung (disorder)\Lung consolidation\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Inflammatory disorder (disorder)\Inflammation of specific body structures or tissue\Inflammation of specific body systems\Inflammatory disorder of the respiratory system (disorder)\Inflammatory disorder of the respiratory tract\Inflammatory disorder of lower respiratory tract\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Inflammatory disorder (disorder)\Inflammation of specific body structures or tissue\Inflammation of specific body organs\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of trunk (disorder)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disorder of soft tissue of thoracic cavity\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of trunk (disorder)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disorder of soft tissue of thoracic cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of trunk (disorder)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disorder of pleura and pleural cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of trunk (disorder)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disease of lung (disorder)\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of trunk (disorder)\Disorder of thoracic segment of trunk\Disorder of thorax (disorder)\Disease of lung (disorder)\Lung consolidation\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of trunk (disorder)\Disorder of soft tissue of trunk\Disorder of soft tissue of thoracic cavity\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of trunk (disorder)\Disorder of soft tissue of trunk\Disorder of soft tissue of thoracic cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of trunk (disorder)\Disorder of soft tissue of body cavity\Disorder of soft tissue of thoracic cavity\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of trunk (disorder)\Disorder of soft tissue of body cavity\Disorder of soft tissue of thoracic cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of connective tissue\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of connective tissue\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Idiopathic disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of soft tissue\Disorder of soft tissue of trunk\Disorder of soft tissue of thoracic cavity\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of soft tissue\Disorder of soft tissue of trunk\Disorder of soft tissue of thoracic cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of soft tissue\Disorder of soft tissue of body cavity\Disorder of soft tissue of thoracic cavity\Interstitial lung disease\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of soft tissue\Disorder of soft tissue of body cavity\Disorder of soft tissue of thoracic cavity\Disorder of pleura\Idiopathic pleuroparenchymal fibroelastosis (disorder)
\Disease\Disorder of soft tissue\Lesion of soft tissue (disorder)\Idiopathic pleuroparenchymal fibroelastosis (disorder)

Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 30-Sep 2021. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module

4634572018 Idiopathic pleuroparenchymal fibroelastosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core

4634573011 Idiopathic pleuropulmonary fibroelastosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core

4634574017 Idiopathic pleuroparenchymal fibroelastosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core

4634575016 IPPFE - idiopathic pleuroparenchymal fibroelastosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core

5399350018 A rare idiopathic interstitial pneumonia characterized by prominent subpleural and parenchymal fibroelastosis and pleural fibrosis, predominantly involving the upper lobes. Signs and symptoms include non-productive cough, dyspnea, and recurrent respiratory infections. Pneumothorax is a frequently reported complication. Pulmonary function test reveals a restrictive pattern and reduced diffusing capacity. Computed tomography shows pleural thickening with signs of fibrosis (traction bronchiectasis, architectural distortion, and loss of volume), and reticulation. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core

5399351019 A rare idiopathic interstitial pneumonia characterised by prominent subpleural and parenchymal fibroelastosis and pleural fibrosis, predominantly involving the upper lobes. Signs and symptoms include non-productive cough, dyspnoea, and recurrent respiratory infections. Pneumothorax is a frequently reported complication. Pulmonary function test reveals a restrictive pattern and reduced diffusing capacity. Computed tomography shows pleural thickening with signs of fibrosis (traction bronchiectasis, architectural distortion, and loss of volume), and reticulation. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core

4634572018 Idiopathic pleuroparenchymal fibroelastosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core

4634573011 Idiopathic pleuropulmonary fibroelastosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core

4634574017 Idiopathic pleuroparenchymal fibroelastosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core

4634575016 IPPFE - idiopathic pleuroparenchymal fibroelastosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core

4634579010 A rare idiopathic interstitial pneumonia with characteristics of prominent subpleural and parenchymal fibroelastosis and pleural fibrosis, predominantly involving the upper lobes. Signs and symptoms include non-productive cough, dyspnea, and recurrent respiratory infections. Pneumothorax is a frequently reported complication. Pulmonary function test reveals a restrictive pattern and reduced diffusing capacity. Computed tomography shows pleural thickening with signs of fibrosis (traction bronchiectasis, architectural distortion and loss of volume) and reticulation. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core

4634580013 A rare idiopathic interstitial pneumonia with characteristics of prominent subpleural and parenchymal fibroelastosis and pleural fibrosis, predominantly involving the upper lobes. Signs and symptoms include non-productive cough, dyspnoea, and recurrent respiratory infections. Pneumothorax is a frequently reported complication. Pulmonary function test reveals a restrictive pattern and reduced diffusing capacity. Computed tomography shows pleural thickening with signs of fibrosis (traction bronchiectasis, architectural distortion and loss of volume) and reticulation. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core

5399350018 A rare idiopathic interstitial pneumonia characterized by prominent subpleural and parenchymal fibroelastosis and pleural fibrosis, predominantly involving the upper lobes. Signs and symptoms include non-productive cough, dyspnea, and recurrent respiratory infections. Pneumothorax is a frequently reported complication. Pulmonary function test reveals a restrictive pattern and reduced diffusing capacity. Computed tomography shows pleural thickening with signs of fibrosis (traction bronchiectasis, architectural distortion, and loss of volume), and reticulation. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core

5399351019 A rare idiopathic interstitial pneumonia characterised by prominent subpleural and parenchymal fibroelastosis and pleural fibrosis, predominantly involving the upper lobes. Signs and symptoms include non-productive cough, dyspnoea, and recurrent respiratory infections. Pneumothorax is a frequently reported complication. Pulmonary function test reveals a restrictive pattern and reduced diffusing capacity. Computed tomography shows pleural thickening with signs of fibrosis (traction bronchiectasis, architectural distortion, and loss of volume), and reticulation. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core

3412731001000118 Pleuroparenchymale Fibroelastose, idiopathische de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module

6287951000241110 fibroélastose pleuroparenchymateuse idiopathique fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module

6287951000241110 fibroélastose pleuroparenchymateuse idiopathique fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module

3412731001000118 Pleuroparenchymale Fibroelastose, idiopathische de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module

Expanded Value Set

Outbound Relationships	Type	Target	Active	Characteristic	Refinability	Group	Values
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Is a	Degenerative disorder	true	Inferred relationship	Existential restriction modifier (core metadata concept)
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Is a	Idiopathic interstitial pneumonitis	false	Inferred relationship	Existential restriction modifier (core metadata concept)
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Is a	Disorder of pleura	true	Inferred relationship	Existential restriction modifier (core metadata concept)
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Finding site	Pleural membrane structure (body structure)	true	Inferred relationship	Existential restriction modifier (core metadata concept)	1
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Associated morphology	Fibrosis (morphologic abnormality)	true	Inferred relationship	Existential restriction modifier (core metadata concept)	1
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Finding site	Structure of interstitial tissue of lung	true	Inferred relationship	Existential restriction modifier (core metadata concept)	2
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Associated morphology	Inflammation and consolidation (morphologic abnormality)	true	Inferred relationship	Existential restriction modifier (core metadata concept)	2
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Finding site	Structure of parenchyma of lung	true	Inferred relationship	Existential restriction modifier (core metadata concept)	3
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Associated morphology	Fibroelastosis (morphologic abnormality)	true	Inferred relationship	Existential restriction modifier (core metadata concept)	3
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Is a	Lung consolidation	true	Inferred relationship	Existential restriction modifier (core metadata concept)
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Is a	Inflammatory disorder of lower respiratory tract	true	Inferred relationship	Existential restriction modifier (core metadata concept)
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Is a	Interstitial lung disease	true	Inferred relationship	Existential restriction modifier (core metadata concept)
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Is a	Inflammation of specific body organs	true	Inferred relationship	Existential restriction modifier (core metadata concept)
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Is a	Idiopathic disease	true	Inferred relationship	Existential restriction modifier (core metadata concept)
Idiopathic pleuroparenchymal fibroelastosis (disorder)	Is a	Lesion of soft tissue (disorder)	true	Inferred relationship	Existential restriction modifier (core metadata concept)

Inbound Relationships

Type

Active

Source

Characteristic

Refinability

Group

Reference Sets

Component annotation with string value reference set (foundation metadata concept)

Back to Start

Id	Description	Lang	Type	Status	Case?	Module
4634572018	Idiopathic pleuroparenchymal fibroelastosis	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
4634573011	Idiopathic pleuropulmonary fibroelastosis	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
4634574017	Idiopathic pleuroparenchymal fibroelastosis (disorder)	en	Fully specified name	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
4634575016	IPPFE - idiopathic pleuroparenchymal fibroelastosis	en	Synonym (core metadata concept)	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core
5399350018	A rare idiopathic interstitial pneumonia characterized by prominent subpleural and parenchymal fibroelastosis and pleural fibrosis, predominantly involving the upper lobes. Signs and symptoms include non-productive cough, dyspnea, and recurrent respiratory infections. Pneumothorax is a frequently reported complication. Pulmonary function test reveals a restrictive pattern and reduced diffusing capacity. Computed tomography shows pleural thickening with signs of fibrosis (traction bronchiectasis, architectural distortion, and loss of volume), and reticulation.	en	Definition	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core
5399351019	A rare idiopathic interstitial pneumonia characterised by prominent subpleural and parenchymal fibroelastosis and pleural fibrosis, predominantly involving the upper lobes. Signs and symptoms include non-productive cough, dyspnoea, and recurrent respiratory infections. Pneumothorax is a frequently reported complication. Pulmonary function test reveals a restrictive pattern and reduced diffusing capacity. Computed tomography shows pleural thickening with signs of fibrosis (traction bronchiectasis, architectural distortion, and loss of volume), and reticulation.	en	Definition	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core
4634572018	Idiopathic pleuroparenchymal fibroelastosis	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
4634573011	Idiopathic pleuropulmonary fibroelastosis	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
4634574017	Idiopathic pleuroparenchymal fibroelastosis (disorder)	en	Fully specified name	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
4634575016	IPPFE - idiopathic pleuroparenchymal fibroelastosis	en	Synonym (core metadata concept)	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core
4634579010	A rare idiopathic interstitial pneumonia with characteristics of prominent subpleural and parenchymal fibroelastosis and pleural fibrosis, predominantly involving the upper lobes. Signs and symptoms include non-productive cough, dyspnea, and recurrent respiratory infections. Pneumothorax is a frequently reported complication. Pulmonary function test reveals a restrictive pattern and reduced diffusing capacity. Computed tomography shows pleural thickening with signs of fibrosis (traction bronchiectasis, architectural distortion and loss of volume) and reticulation.	en	Definition	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core
4634580013	A rare idiopathic interstitial pneumonia with characteristics of prominent subpleural and parenchymal fibroelastosis and pleural fibrosis, predominantly involving the upper lobes. Signs and symptoms include non-productive cough, dyspnoea, and recurrent respiratory infections. Pneumothorax is a frequently reported complication. Pulmonary function test reveals a restrictive pattern and reduced diffusing capacity. Computed tomography shows pleural thickening with signs of fibrosis (traction bronchiectasis, architectural distortion and loss of volume) and reticulation.	en	Definition	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core
5399350018	A rare idiopathic interstitial pneumonia characterized by prominent subpleural and parenchymal fibroelastosis and pleural fibrosis, predominantly involving the upper lobes. Signs and symptoms include non-productive cough, dyspnea, and recurrent respiratory infections. Pneumothorax is a frequently reported complication. Pulmonary function test reveals a restrictive pattern and reduced diffusing capacity. Computed tomography shows pleural thickening with signs of fibrosis (traction bronchiectasis, architectural distortion, and loss of volume), and reticulation.	en	Definition	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core
5399351019	A rare idiopathic interstitial pneumonia characterised by prominent subpleural and parenchymal fibroelastosis and pleural fibrosis, predominantly involving the upper lobes. Signs and symptoms include non-productive cough, dyspnoea, and recurrent respiratory infections. Pneumothorax is a frequently reported complication. Pulmonary function test reveals a restrictive pattern and reduced diffusing capacity. Computed tomography shows pleural thickening with signs of fibrosis (traction bronchiectasis, architectural distortion, and loss of volume), and reticulation.	en	Definition	Active	Entire term case sensitive (core metadata concept)	SNOMED CT core
3412731001000118	Pleuroparenchymale Fibroelastose, idiopathische	de	Synonym (core metadata concept)	Active	Entire term case sensitive (core metadata concept)	SNOMED CT Switzerland NRC maintained Module
6287951000241110	fibroélastose pleuroparenchymateuse idiopathique	fr	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT Switzerland NRC maintained Module
6287951000241110	fibroélastose pleuroparenchymateuse idiopathique	fr	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT Switzerland NRC maintained Module
3412731001000118	Pleuroparenchymale Fibroelastose, idiopathische	de	Synonym (core metadata concept)	Active	Entire term case sensitive (core metadata concept)	SNOMED CT Switzerland NRC maintained Module