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1963002: Paroxysmal nocturnal hemoglobinuria (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2002. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
4387014 Paroxysmal nocturnal hemoglobinuria en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
4388016 Marchiafava-Micheli syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
479750016 Paroxysmal nocturnal haemoglobinuria en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
747959018 Paroxysmal nocturnal hemoglobinuria (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
5244076012 PNH - paroxysmal nocturnal hemoglobinuria en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
5244077015 PNH - paroxysmal nocturnal haemoglobinuria en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
4387014 Paroxysmal nocturnal hemoglobinuria en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
4387014 Paroxysmal nocturnal hemoglobinuria en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
4388016 Marchiafava-Micheli syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
4389012 PNH en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
479750016 Paroxysmal nocturnal haemoglobinuria en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
479750016 Paroxysmal nocturnal haemoglobinuria en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
747959018 Paroxysmal nocturnal hemoglobinuria (disorder) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
747959018 Paroxysmal nocturnal hemoglobinuria (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
1216091016 PNH - Paroxysmal nocturnal haemoglobinuria en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
1216091016 PNH - Paroxysmal nocturnal haemoglobinuria en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
1217598012 PNH - Paroxysmal nocturnal hemoglobinuria en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
1217598012 PNH - Paroxysmal nocturnal hemoglobinuria en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
5244076012 PNH - paroxysmal nocturnal hemoglobinuria en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
5244077015 PNH - paroxysmal nocturnal haemoglobinuria en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3444171001000119 Hämoglobinurie, nächtliche paroxysmale de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
877851000172112 HPN - hémoglobinurie paroxystique nocturne fr Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
910001000172116 hémoglobinurie paroxystique nocturne fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
877851000172112 HPN - hémoglobinurie paroxystique nocturne fr Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
910001000172116 hémoglobinurie paroxystique nocturne fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3444171001000119 Hämoglobinurie, nächtliche paroxysmale de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Paroxysmal nocturnal haemoglobinuria Is a Anaemia due to intrinsic red cell abnormality true Inferred relationship Existential restriction modifier (core metadata concept)
Paroxysmal nocturnal haemoglobinuria Finding site Erythrocyte false Inferred relationship Existential restriction modifier (core metadata concept)
Paroxysmal nocturnal haemoglobinuria Finding site Hematopoietic system structure false Inferred relationship Existential restriction modifier (core metadata concept)
Paroxysmal nocturnal haemoglobinuria Onset Sudden false Inferred relationship Existential restriction modifier (core metadata concept)
Paroxysmal nocturnal haemoglobinuria Onset Sudden onset (contextual qualifier) (qualifier value) false Inferred relationship Existential restriction modifier (core metadata concept)
Paroxysmal nocturnal haemoglobinuria Has definitional manifestation érythropénie false Inferred relationship Existential restriction modifier (core metadata concept)
Paroxysmal nocturnal haemoglobinuria Finding site Hematopoietic system structure false Inferred relationship Existential restriction modifier (core metadata concept)
Paroxysmal nocturnal haemoglobinuria Has interpretation Below reference range false Inferred relationship Existential restriction modifier (core metadata concept) 1
Paroxysmal nocturnal haemoglobinuria Interprets Measurement of total haemoglobin concentration false Inferred relationship Existential restriction modifier (core metadata concept) 1
Paroxysmal nocturnal haemoglobinuria Has interpretation Below reference range false Inferred relationship Existential restriction modifier (core metadata concept) 2
Paroxysmal nocturnal haemoglobinuria Interprets Red blood cell count false Inferred relationship Existential restriction modifier (core metadata concept) 2

Inbound Relationships Type Active Source Characteristic Refinability Group
Thrombophilia due to paroxysmal nocturnal haemoglobinuria Due to True Paroxysmal nocturnal haemoglobinuria Inferred relationship Existential restriction modifier (core metadata concept) 1
Occlusion of microvasculature of skin due to paroxysmal nocturnal haemoglobinuria-associated platelet plugs Due to True Paroxysmal nocturnal haemoglobinuria Inferred relationship Existential restriction modifier (core metadata concept) 2

This concept is not in any reference sets

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