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20415001: Progressive sclerosing poliodystrophy (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2002. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
34333011 Progressive sclerosing poliodystrophy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
34334017 Alpers' disease en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
34335016 Gray matter degeneration en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
34336015 Spongy glioneuronal dystrophy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
34338019 Poliodystrophy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
749555010 Progressive sclerosing poliodystrophy (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
1222436018 Progressive neuronal degeneration with liver cirrhosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
1222437010 Alper's disease en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3799791012 Grey matter degeneration en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
34333011 Progressive sclerosing poliodystrophy en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
34333011 Progressive sclerosing poliodystrophy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
34334017 Alpers' disease en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
34335016 Gray matter degeneration en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
34335016 Gray matter degeneration en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
34336015 Spongy glioneuronal dystrophy en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
34336015 Spongy glioneuronal dystrophy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
34338019 Poliodystrophy en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
34338019 Poliodystrophy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
749555010 Progressive sclerosing poliodystrophy (disorder) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
749555010 Progressive sclerosing poliodystrophy (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
1222436018 Progressive neuronal degeneration with liver cirrhosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
1222436018 Progressive neuronal degeneration with liver cirrhosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
1222437010 Alper's disease en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
1222437010 Alper's disease en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3799791012 Grey matter degeneration en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3424221001000113 Alpers-Huttenlocher-Syndrom de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
272041000077116 poliodystrophie sclérosante progressive fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
272041000077116 poliodystrophie sclérosante progressive fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3424221001000113 Alpers-Huttenlocher-Syndrom de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Progressive sclerosing poliodystrophy Is a Disorder of cerebral cortex (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
Progressive sclerosing poliodystrophy Is a Progressive neuronal degeneration of childhood true Inferred relationship Existential restriction modifier (core metadata concept)
Progressive sclerosing poliodystrophy Is a Degenerative brain disorder false Inferred relationship Existential restriction modifier (core metadata concept)
Progressive sclerosing poliodystrophy Is a Hereditary degenerative disease of central nervous system true Inferred relationship Existential restriction modifier (core metadata concept)
Progressive sclerosing poliodystrophy Finding site Cerebral cortex false Inferred relationship Existential restriction modifier (core metadata concept) 2
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 2
Progressive sclerosing poliodystrophy Finding site Structure of central nervous system false Inferred relationship Existential restriction modifier (core metadata concept) 2
Progressive sclerosing poliodystrophy Occurrence Childhood false Inferred relationship Existential restriction modifier (core metadata concept) 3
Progressive sclerosing poliodystrophy Finding site Gray matter structure of central nervous system true Inferred relationship Existential restriction modifier (core metadata concept) 1
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 2
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 1
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 1
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 1
Progressive sclerosing poliodystrophy Is a Polioencephalopathy (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 1
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 2
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 2
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 1
Progressive sclerosing poliodystrophy Is a Cerebral degeneration in childhood false Inferred relationship Existential restriction modifier (core metadata concept)
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 2
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 1
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 2
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 1
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 1
Progressive sclerosing poliodystrophy Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept) 2
Progressive sclerosing poliodystrophy Associated morphology Degenerative abnormality (morphologic abnormality) false Inferred relationship Existential restriction modifier (core metadata concept) 2
Progressive sclerosing poliodystrophy Associated morphology Degenerative abnormality (morphologic abnormality) true Inferred relationship Existential restriction modifier (core metadata concept) 1
Progressive sclerosing poliodystrophy Occurrence Childhood true Inferred relationship Existential restriction modifier (core metadata concept) 1

Inbound Relationships Type Active Source Characteristic Refinability Group

This concept is not in any reference sets

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