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253335001: Isomerism of atrial appendages (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2002. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
377267018 Isomerism of atrial appendages en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
644083018 Isomerism of atrial appendages (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
377267018 Isomerism of atrial appendages en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
377267018 Isomerism of atrial appendages en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
644083018 Isomerism of atrial appendages (disorder) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
644083018 Isomerism of atrial appendages (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
5071531000241118 isomérie des appendices auriculaires fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
5071531000241118 isomérie des appendices auriculaires fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


3 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Isomerism of atrial appendages Is a Congenital abnormality of atria and atrial septum false Inferred relationship Existential restriction modifier (core metadata concept)
Isomerism of atrial appendages Associated morphology anomalie congénitale false Inferred relationship Existential restriction modifier (core metadata concept) 1
Isomerism of atrial appendages Finding site Cardiovascular system subdivision false Inferred relationship Existential restriction modifier (core metadata concept) 2
Isomerism of atrial appendages Finding site Atrial structure true Inferred relationship Existential restriction modifier (core metadata concept) 1
Isomerism of atrial appendages Occurrence Congenital false Inferred relationship Existential restriction modifier (core metadata concept)
Isomerism of atrial appendages Finding site Structure of cardiovascular system (body structure) false Inferred relationship Existential restriction modifier (core metadata concept) 2
Isomerism of atrial appendages Finding site Atrial structure false Inferred relationship Existential restriction modifier (core metadata concept) 1
Isomerism of atrial appendages Associated morphology anomalie congénitale false Inferred relationship Existential restriction modifier (core metadata concept) 1
Isomerism of atrial appendages Is a Congenital heart disease (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
Isomerism of atrial appendages Occurrence Congenital false Inferred relationship Existential restriction modifier (core metadata concept) 2
Isomerism of atrial appendages Associated morphology anomalie du développement false Inferred relationship Existential restriction modifier (core metadata concept) 2
Isomerism of atrial appendages Finding site Heart structure false Inferred relationship Existential restriction modifier (core metadata concept) 2
Isomerism of atrial appendages Occurrence Congenital false Inferred relationship Existential restriction modifier (core metadata concept) 3
Isomerism of atrial appendages Associated morphology anomalie du développement false Inferred relationship Existential restriction modifier (core metadata concept) 3
Isomerism of atrial appendages Finding site Atrial structure false Inferred relationship Existential restriction modifier (core metadata concept) 3
Isomerism of atrial appendages Occurrence Congenital true Inferred relationship Existential restriction modifier (core metadata concept) 1
Isomerism of atrial appendages Is a Congenital anomaly of cardiac chamber (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
Isomerism of atrial appendages Associated morphology Morphologically abnormal structure true Inferred relationship Existential restriction modifier (core metadata concept) 1
Isomerism of atrial appendages Pathological process (attribute) Pathological developmental process (qualifier value) true Inferred relationship Existential restriction modifier (core metadata concept) 1
Isomerism of atrial appendages Is a Congenital abnormality of atrium (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)

Inbound Relationships Type Active Source Characteristic Refinability Group
A rare heterotaxia characterised by complex congenital heart malformations and abnormal lateralisation of other thoracic and abdominal organs due to embryonic disruption of the left-right axis development. Cardiac defects include dextrocardia or mesocardia, common atrioventricular valve associated with complete atrioventricular septal defect or common atrium, transposition or malposition of the great arteries, and total anomalous pulmonary venous drainage, among others. Cardiac arrhythmias are frequently observed. Typical abnormalities of other organs are bilateral trilobed lungs, midline liver, and asplenia. Patients present in the newborn period with severe cardiac failure and cyanosis. Prognosis is poor. Is a True Isomerism of atrial appendages Inferred relationship Existential restriction modifier (core metadata concept)
Isomerism of left atrial appendage (disorder) Is a True Isomerism of atrial appendages Inferred relationship Existential restriction modifier (core metadata concept)
Mirror imaged atria Is a True Isomerism of atrial appendages Inferred relationship Existential restriction modifier (core metadata concept)

This concept is not in any reference sets

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