Inbound Relationships |
Type |
Active |
Source |
Characteristic |
Refinability |
Group |
Lymphoproliferative disorder following transplantation |
Is a |
False |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Plasma cell disorder |
Is a |
False |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Atypical lymphoproliferative disorder |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Acute lymphoid leukemia, disease (disorder) |
Is a |
False |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Chronic lymphoid leukemia, disease |
Is a |
False |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Multiple myeloma and immunoproliferative disease |
Is a |
False |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Lymphoreticular tumor (disorder) |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Immunoproliferative disorder (disorder) |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Hemolytic anemia associated with lymphoproliferative disorder |
Associated with |
False |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
X-linked immunodeficiency with magnesium defect, Epstein-Barr virus infection and neoplasia |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Lymphoproliferative disorder after transplantation of bone marrow |
Is a |
False |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Dianzani autoimmune lymphoproliferative disease (DALD) is a very rare disorder characterized by autoimmunity, lymphadenopathy and/or splenomegaly. |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Natural killer cell enteropathy (disorder) |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
RAS-associated autoimmune leukoproliferative disease (disorder) |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Chronic cold agglutinin disease associated with B-cell neoplasm (disorder) |
Due to |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
9 |
Secondary autoimmune hemolytic anemia co-occurrent and due to lymphoproliferative disorder |
Due to |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Secondary autoimmune hemolytic anemia co-occurrent and due to lymphoproliferative disorder |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Persistent polyclonal B-cell lymphocytosis (PPBL) is a rare, generally benign, lymphoproliferative hematological disease characterized by chronic, stable, persistent, polyclonal lymphocytosis of memory B-cell origin, the presence of binucleated lymphocytes in the peripheral blood, and a polyclonal increase in serum immunoglobulin M (IgM). Patients are most frequently asymptomatic or may present with mild splenomegaly. |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Acquired angioedema due to activation of the classical complement pathway related to an underlying lymphoreticular disorder particularly lymphoma or monoclonal gammopathy of unknown significance (MGUS) |
Due to |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Acquired angioedema due to activation of the classical complement pathway related to an underlying lymphoreticular disorder particularly lymphoma or monoclonal gammopathy of unknown significance (MGUS) |
Is a |
False |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Lymphoproliferative disorder caused by methotrexate |
Is a |
False |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Autosomal recessive lymphoproliferative disease (disorder) |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Iatrogenic immunodeficiency-associated lymphoproliferative disorder (disorder) |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Cutaneous CD30+ lymphoproliferative disorder |
Is a |
False |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Hydroa vacciniforme-like lymphoma (disorder) |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Primary cutaneous CD30 antigen positive T-cell lymphoproliferative disorder |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Vasculitis due to lymphoproliferative disorder |
Due to |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Hydroa vacciniforme-like cutaneous T-cell lymphoma |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Autoimmune lymphoproliferative syndrome |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
A rare immune dysregulation disease with immunodeficiency characterised by infantile or childhood onset of a variable phenotype including recurrent/persistent bacterial, fungal, and viral infections with involvement of the skin, lower respiratory tract, and gastrointestinal tract, eczema, allergies, and inflammatory bowel disease, among others. EBV-related smooth muscle tumours have also been reported. Immunophenotyping shows decreased Treg counts, as well as a deficient CD3/CD28 co-stimulation response in CD4+ and CD8+ T-cells. |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Combined immunodeficiency due to interleukin-2 inducible T cell kinase deficiency (disorder) |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
A rare autosomal recessive primary immunodeficiency characterized by susceptibility to Epstein-Barr virus (EBV)-related disorders (B-cell lymphoproliferative disorders including Hodgkin lymphoma) as well as dysgammaglobulinemia and recurrent infections. Patients can present with recurrent fever, lymphadenopathy, hepatosplenomegaly, Behçet-like stomatitis, pharyngitis, tonsillitis, adenitis, and viral encephalitis. |
Is a |
True |
Lymphoproliferative disorder |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|