FHIR © HL7.org  |  Server Home  |  FHIR Server FHIR Server 3.7.4-SNAPSHOT  |  FHIR Version n/a  User: [n/a]

277466009: Lymphoproliferative disorder (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2002. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
413994012 Lymphoproliferative disorder en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
670505016 Lymphoproliferative disorder (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
413994012 Lymphoproliferative disorder en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
413994012 Lymphoproliferative disorder en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
670505016 Lymphoproliferative disorder (disorder) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
670505016 Lymphoproliferative disorder (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
40281000188116 syndrome lymphoprolifératif fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
130461000077112 trouble lymphoprolifératif fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
40281000188116 syndrome lymphoprolifératif fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
130461000077112 trouble lymphoprolifératif fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


628 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Lymphoproliferative disorder Is a Malignant white blood cell disorder false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder Pathological process Neoplastic process false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder Finding site Lymphoid system structure false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder Associated morphology néoplasie maligne (morphologie) false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder Finding site Hematopoietic system structure false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder Pathological process Malignant neoplastic process false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder Finding site Leucocyte false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder Is a White blood cell disorder false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder Is a Disorder of lymphoid system (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder Finding site Lymphocytic tissue structure false Inferred relationship Existential restriction modifier (core metadata concept) 1
Lymphoproliferative disorder Associated morphology Proliferation false Inferred relationship Existential restriction modifier (core metadata concept) 1
Lymphoproliferative disorder Finding site Hematopoietic system structure false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder Associated morphology White blood cell abnormality (morphologic abnormality) false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder Is a Disorder of hematopoietic morphology true Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder Associated morphology Lymphoproliferative disorder true Inferred relationship Existential restriction modifier (core metadata concept) 1

Inbound Relationships Type Active Source Characteristic Refinability Group
Lymphoproliferative disorder following transplantation Is a False Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Plasma cell disorder Is a False Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Atypical lymphoproliferative disorder Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Acute lymphoid leukemia, disease (disorder) Is a False Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Chronic lymphoid leukemia, disease Is a False Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Multiple myeloma and immunoproliferative disease Is a False Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoreticular tumor (disorder) Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Immunoproliferative disorder (disorder) Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Hemolytic anemia associated with lymphoproliferative disorder Associated with False Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
X-linked immunodeficiency with magnesium defect, Epstein-Barr virus infection and neoplasia Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder after transplantation of bone marrow Is a False Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Dianzani autoimmune lymphoproliferative disease (DALD) is a very rare disorder characterized by autoimmunity, lymphadenopathy and/or splenomegaly. Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Natural killer cell enteropathy (disorder) Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
RAS-associated autoimmune leukoproliferative disease (disorder) Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Chronic cold agglutinin disease associated with B-cell neoplasm (disorder) Due to True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept) 9
Secondary autoimmune hemolytic anemia co-occurrent and due to lymphoproliferative disorder Due to True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept) 2
Secondary autoimmune hemolytic anemia co-occurrent and due to lymphoproliferative disorder Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Persistent polyclonal B-cell lymphocytosis (PPBL) is a rare, generally benign, lymphoproliferative hematological disease characterized by chronic, stable, persistent, polyclonal lymphocytosis of memory B-cell origin, the presence of binucleated lymphocytes in the peripheral blood, and a polyclonal increase in serum immunoglobulin M (IgM). Patients are most frequently asymptomatic or may present with mild splenomegaly. Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Acquired angioedema due to activation of the classical complement pathway related to an underlying lymphoreticular disorder particularly lymphoma or monoclonal gammopathy of unknown significance (MGUS) Due to True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept) 2
Acquired angioedema due to activation of the classical complement pathway related to an underlying lymphoreticular disorder particularly lymphoma or monoclonal gammopathy of unknown significance (MGUS) Is a False Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Lymphoproliferative disorder caused by methotrexate Is a False Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Autosomal recessive lymphoproliferative disease (disorder) Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Iatrogenic immunodeficiency-associated lymphoproliferative disorder (disorder) Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Cutaneous CD30+ lymphoproliferative disorder Is a False Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Hydroa vacciniforme-like lymphoma (disorder) Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Primary cutaneous CD30 antigen positive T-cell lymphoproliferative disorder Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Vasculitis due to lymphoproliferative disorder Due to True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept) 2
Hydroa vacciniforme-like cutaneous T-cell lymphoma Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Autoimmune lymphoproliferative syndrome Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
A rare immune dysregulation disease with immunodeficiency characterised by infantile or childhood onset of a variable phenotype including recurrent/persistent bacterial, fungal, and viral infections with involvement of the skin, lower respiratory tract, and gastrointestinal tract, eczema, allergies, and inflammatory bowel disease, among others. EBV-related smooth muscle tumours have also been reported. Immunophenotyping shows decreased Treg counts, as well as a deficient CD3/CD28 co-stimulation response in CD4+ and CD8+ T-cells. Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
Combined immunodeficiency due to interleukin-2 inducible T cell kinase deficiency (disorder) Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)
A rare autosomal recessive primary immunodeficiency characterized by susceptibility to Epstein-Barr virus (EBV)-related disorders (B-cell lymphoproliferative disorders including Hodgkin lymphoma) as well as dysgammaglobulinemia and recurrent infections. Patients can present with recurrent fever, lymphadenopathy, hepatosplenomegaly, Behçet-like stomatitis, pharyngitis, tonsillitis, adenitis, and viral encephalitis. Is a True Lymphoproliferative disorder Inferred relationship Existential restriction modifier (core metadata concept)

This concept is not in any reference sets

Back to Start