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281833003: Entire hematological system (body structure)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2002. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
2528953015 Entire hematological system (body structure) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
2532372011 Entire haematological system en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
2532373018 Entire hematological system en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
419941014 Haematological system en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
419942019 Hematological system en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
675417019 Hematological system (body structure) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
2528953015 Entire hematological system (body structure) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
2528953015 Entire hematological system (body structure) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
2532372011 Entire haematological system en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
2532372011 Entire haematological system en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
2532373018 Entire hematological system en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
2532373018 Entire hematological system en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Entire hematological system (body structure) Is a Body system structure false Inferred relationship Existential restriction modifier (core metadata concept)
Entire hematological system (body structure) partie de Entire body as a whole (body structure) false Additional relationship (core metadata concept) Existential restriction modifier (core metadata concept)
Entire hematological system (body structure) Is a Hematological system structure (body structure) true Inferred relationship Existential restriction modifier (core metadata concept)

Inbound Relationships Type Active Source Characteristic Refinability Group
Intentional coumarin overdose Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Coumarin overdose of undetermined intent Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Accidental warfarin overdose Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
surdose intentionnelle de warfarine sodique Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
surdose de warfarin d'intention indéterminée Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Factor V Leiden mutation Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Homozygous Factor V Leiden mutation Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Heterozygous Factor V Leiden mutation (disorder) Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Idiopathic factor VIII deficiency Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Autoimmune factor VIII deficiency Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Pregnancy-related factor VIII deficiency Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Malignancy-related factor VIII deficiency Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Antibody screen Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Hemolysin detection, cold (procedure) Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Hemolysin detection, warm Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Acquired factor IX deficiency disease Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
RBC antibody detection, warm with titration Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Blood coagulation disorder with shortened coagulation time Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Blood coagulation disorder with prolonged coagulation time Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Blood coagulation disorder with shortened bleeding time Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Blood coagulation disorder with prolonged bleeding time Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Blood coagulation disorder with impaired clot retraction time (disorder) Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Deficiency of pyruvate kinase Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Deficiency of adenylate kinase Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
von Willebrand disease, type IIF Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Hemorrhagic disease of the newborn due to vitamin K deficiency Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Infusion of dextran (procedure) Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Hb S disease Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Sickle cell-beta-thalassaemia Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Sickle cell beta plus thalassaemia Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Sickle cell-beta^0^-thalassemia (disorder) Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Sickle cell-delta beta^0^-thalassemia Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Sickle cell trait with coexistent alpha-thalassemia (disorder) Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Sickle cell-haemoglobin Lepore disease Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Sickle cell-Hemoglobin O Arab disease Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Apheresis Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 2
Blood coagulation disorder, categorized by value of screening test Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
von Willebrand disorder Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
A form of von Willebrand disease (VWD) with characteristics of a bleeding disorder associated with a partial, quantitative plasmatic deficiency of an otherwise structurally and functionally normal von Willebrand factor (VWF). The type 1 disease is considered to be the most common form of VWD, caused by mutations in the VWF gene (12p13.3). Transmitted in an autosomal dominant manner. Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Hereditary von Willebrand disease type 2 Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
A total or near-total absence of Willebrand factor (VWF) in the plasma and cellular compartments leading to a profound deficiency of plasmatic factor VIII (FVIII). It is the most severe form of von Willebrand disease. Onset usually occurs during the neonatal period or in infancy, but later onset has been reported. The disease is caused by homozygous or compound heterozygous mutations (mainly missense or large mutations) in the VWF gene (12p13.3) that lead to synthesis of a truncated protein or allele silencing. The pattern of inheritance is autosomal recessive. Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Hereditary von Willebrand disease type 1B (disorder) Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Hereditary von Willebrand disease type 1C Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Pseudo von Willebrand disease Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Vitamin K deficiency coagulation disorder Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Hereditary von Willebrand disease type 1A (disorder) Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
von Willebrand disease, type 1^a^ Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
von Willebrand disease type IA Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Hereditary von Willebrand disease type 2A Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Von-Willebrand-Syndrom Typ 2A Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Hereditary von Willebrand disease type 2B Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
maladie de von Willebrand type 2B Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Acquired hypofibrinogenemia Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Hereditary von Willebrand disease type 2M (disorder) Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Fibrinogen deficiency Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
maladie de von Willebrand type 2M Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Acquired afibrinogenemia (disorder) Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Hereditary von Willebrand disease type 2N (disorder) Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
von Willebrand disease Normandy Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Antibody identification, RBC, albumin Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Chronic idiopathic thrombocytopenic purpura Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Hemolysin detection, cold, quantitative Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Purpura fulminans Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Anti-human globulin test, enzyme technique, titer Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Factor XIII inhibitor disorder Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Acquired factor VIII deficiency disease Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Acquired factor XII deficiency disease (disorder) Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Protein S deficiency disease Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
dermatite ocra di Favre Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Stasis purpura Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Vitamin B12 absorption test (procedure) Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Vitamin B12 isotope studies Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 2
Indirect Coombs test Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Drug-induced coagulation inhibitor disorder Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Severe hereditary factor VIII deficiency disease (disorder) Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Hereditary coagulation factor deficiency Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Compatibility test, crossmatch, screening for compatible unit, saline and/or high protein Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Blood unit collection for directed donation, donor Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Fresh frozen plasma preparation Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
RBC antibody detection, cold with titration Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Factor XIII deficiency disease Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Packed RBC preparation, sedimentation Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
RBC antibody detection with saline Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
von Willebrand disease, type IIC Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Lupus anticoagulant disorder Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
von Willebrand disease, type IIB Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Therapeutic plasmapheresis using plasma as the major replacement fluid (procedure) Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 2
Blood typing, ABO, Rho(D) and RBC antibody screening Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Pigmented purpuric lichenoid dermatitis of Gougerot and Blum (disorder) Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Acquired factor VII deficiency disease Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Red cell iron utilisation study Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Antibody detection, RBC, saline, high protein and anti-human globulin technique Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Plasmapheresis Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 2
Vascular haemostatic disease Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Allergic purpura Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Blood group typing B Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Miscarriage with afibrinogenaemia Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Plasma radioiron turnover rate Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Hemoglobin S disease without crisis Finding site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept) 1
Blood donor rejection, clerical Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)
Antibody detection, RBC, enzyme, 1 stage technique, including anti-human globulin Procedure site False Entire hematological system (body structure) Inferred relationship Existential restriction modifier (core metadata concept)

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