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33374000: Familial hemophagocytic lymphohistiocytosis (disorder)


    Status: retired, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2003. Module: SNOMED CT core

    Descriptions:

    Id Description Lang Type Status Case? Module
    55698014 Familial hemophagocytic histiocytosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    197010011 Familial erythrophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    197011010 Familial hemophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    485499018 Omenn's syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
    485500010 Familial histiocytic reticulosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    485501014 FEL - Familial erythrophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
    485502019 Familial haemophagocytic histiocytosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    485503012 Familial haemophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    485504018 FHL - Familial haemophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
    485505017 Familial haemophagocytic reticulosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    485506016 Familial hemophagocytic reticulosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    485507013 FHL - Familial hemophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
    764770016 Familial hemophagocytic lymphohistiocytosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
    55698014 Familial hemophagocytic histiocytosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
    55698014 Familial hemophagocytic histiocytosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    197010011 Familial erythrophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
    197010011 Familial erythrophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    197011010 Familial hemophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
    197011010 Familial hemophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    485499018 Omenn's syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
    485500010 Familial histiocytic reticulosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
    485500010 Familial histiocytic reticulosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    485501014 FEL - Familial erythrophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
    485502019 Familial haemophagocytic histiocytosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
    485502019 Familial haemophagocytic histiocytosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    485503012 Familial haemophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
    485503012 Familial haemophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    485504018 FHL - Familial haemophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
    485505017 Familial haemophagocytic reticulosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
    485505017 Familial haemophagocytic reticulosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    485506016 Familial hemophagocytic reticulosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
    485506016 Familial hemophagocytic reticulosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    485507013 FHL - Familial hemophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
    485507013 FHL - Familial hemophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
    764770016 Familial hemophagocytic lymphohistiocytosis (disorder) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
    764770016 Familial hemophagocytic lymphohistiocytosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core


    0 descendants.

    Expanded Value Set


    Outbound Relationships Type Target Active Characteristic Refinability Group Values
    Familial hemophagocytic lymphohistiocytosis Is a Hemophagocytic syndrome false Inferred relationship Existential restriction modifier (core metadata concept)
    Familial hemophagocytic lymphohistiocytosis Is a Atypical lymphoproliferative disorder false Inferred relationship Existential restriction modifier (core metadata concept)
    Familial hemophagocytic lymphohistiocytosis Is a Haemolytic erythrophagocytic syndrome false Inferred relationship Existential restriction modifier (core metadata concept)
    Familial hemophagocytic lymphohistiocytosis Associated morphology néoplasie maligne (morphologie) false Inferred relationship Existential restriction modifier (core metadata concept)
    Familial hemophagocytic lymphohistiocytosis Finding site Lymphoid system structure false Inferred relationship Existential restriction modifier (core metadata concept)
    Familial hemophagocytic lymphohistiocytosis Finding site Leucocyte false Inferred relationship Existential restriction modifier (core metadata concept)
    Familial hemophagocytic lymphohistiocytosis Associated morphology Histiocytosis false Inferred relationship Existential restriction modifier (core metadata concept) 1
    Familial hemophagocytic lymphohistiocytosis Associated morphology Immunoproliferative morphology false Inferred relationship Existential restriction modifier (core metadata concept) 3
    Familial hemophagocytic lymphohistiocytosis Finding site Entire hematological system (body structure) false Inferred relationship Existential restriction modifier (core metadata concept) 1
    Familial hemophagocytic lymphohistiocytosis Pathological process Neoplastic process false Inferred relationship Existential restriction modifier (core metadata concept)
    Familial hemophagocytic lymphohistiocytosis Finding site Hematopoietic system structure false Inferred relationship Existential restriction modifier (core metadata concept)
    Familial hemophagocytic lymphohistiocytosis Pathological process Malignant neoplastic process false Inferred relationship Existential restriction modifier (core metadata concept)
    Familial hemophagocytic lymphohistiocytosis Finding site Lymphocytic tissue structure false Inferred relationship Existential restriction modifier (core metadata concept) 2
    Familial hemophagocytic lymphohistiocytosis Associated morphology Proliferation false Inferred relationship Existential restriction modifier (core metadata concept) 2
    Familial hemophagocytic lymphohistiocytosis Finding site Structure of immune system (body structure) false Inferred relationship Existential restriction modifier (core metadata concept) 3

    Inbound Relationships Type Active Source Characteristic Refinability Group

    Reference Sets

    Concept inactivation indicator attribute value reference set (foundation metadata concept)

    POSSIBLY EQUIVALENT TO association reference set

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