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403519001: Poikiloderma due to scleroderma (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 01-Jan 2024. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
1782553012 Scleroderma-associated poikiloderma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
1787788017 Poikiloscleroderma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5288054013 Poikiloderma due to scleroderma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5288055014 Poikiloderma due to scleroderma (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
1771445013 Scleroderma-associated poikiloderma (disorder) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
1771445013 Scleroderma-associated poikiloderma (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
1782553012 Scleroderma-associated poikiloderma en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
1782553012 Scleroderma-associated poikiloderma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
1787787010 Poikiloderma due to systemic sclerosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
1787787010 Poikiloderma due to systemic sclerosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
1787788017 Poikiloscleroderma en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
1787788017 Poikiloscleroderma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5288054013 Poikiloderma due to scleroderma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5288055014 Poikiloderma due to scleroderma (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Poikiloderma due to scleroderma Is a Poikiloderma (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)
Poikiloderma due to scleroderma Is a Cutaneous complication of systemic sclerosis (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
Poikiloderma due to scleroderma Is a Degenerative disorder of musculoskeletal system (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
Poikiloderma due to scleroderma Finding site Structure of fascia (body structure) false Inferred relationship Existential restriction modifier (core metadata concept) 1
Poikiloderma due to scleroderma Associated morphology dégénérescence false Inferred relationship Existential restriction modifier (core metadata concept)
Poikiloderma due to scleroderma Associated morphology Sclerosis (morphologic abnormality) false Inferred relationship Existential restriction modifier (core metadata concept) 1
Poikiloderma due to scleroderma Finding site Skin and/or subcutaneous tissue structure (body structure) false Inferred relationship Existential restriction modifier (core metadata concept)
Poikiloderma due to scleroderma Associated with Systemic sclerosis false Inferred relationship Existential restriction modifier (core metadata concept) 2
Poikiloderma due to scleroderma Finding site Skin structure false Inferred relationship Existential restriction modifier (core metadata concept) 1
Poikiloderma due to scleroderma Associated morphology Poikiloderma false Inferred relationship Existential restriction modifier (core metadata concept) 1
Poikiloderma due to scleroderma Finding site Skin structure true Inferred relationship Existential restriction modifier (core metadata concept) 1
Poikiloderma due to scleroderma Associated morphology Poikiloderma true Inferred relationship Existential restriction modifier (core metadata concept) 1
Poikiloderma due to scleroderma Due to A rare autoimmune connective tissue disorder characterized by abnormal hardening of the skin and sometimes other organs. It is classified into two main forms: localized scleroderma and systemic sclerosis (SSc), the latter comprising three subsets; diffuse cutaneous SSc (dcSSc), limited cutaneous SSc (lcSSc) and limited SSc (lSSc). Localized scleroderma is the cutaneous form of scleroderma characterized by fibrosis of the skin causing cutaneous plaques (morphea) or strips (linear scleroderma). Systemic sclerosis (SSc) is a generalized disorder characterized by fibrosis and vascular obliteration in the skin and organs, particularly, lungs, heart, and digestive tract. The exact cause of scleroderma is unknown. The disease originates from an autoimmune reaction, which leads to localized overproduction of collagen. In some cases, the condition is associated with exposure to chemicals. Other suggested causes include genetic and infectious mechanisms. true Inferred relationship Existential restriction modifier (core metadata concept) 2

Inbound Relationships Type Active Source Characteristic Refinability Group

This concept is not in any reference sets

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