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403546006: Lymphangiomatosis (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2020. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
1771472017 Lymphangiomatosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
1782571017 Lymphangiomatosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
1771472017 Lymphangiomatosis (disorder) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
1771472017 Lymphangiomatosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
1782571017 Lymphangiomatosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
1782571017 Lymphangiomatosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5263741000241117 lymphangiomatose fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
5263741000241117 lymphangiomatose fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


2 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Lymphangiomatosis Is a Congenital lymphangioma (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphangiomatosis Finding site Structure of lymphatic vessel false Inferred relationship Existential restriction modifier (core metadata concept) 1
Lymphangiomatosis Associated morphology Lymphatic vessel tumour false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphangiomatosis Associated morphology Congenital lymphatic malformation false Inferred relationship Existential restriction modifier (core metadata concept) 1
Lymphangiomatosis Occurrence Congenital false Inferred relationship Existential restriction modifier (core metadata concept)
Lymphangiomatosis Finding site Structure of lymphatic vessel false Inferred relationship Existential restriction modifier (core metadata concept) 1
Lymphangiomatosis Associated morphology Congenital lymphatic malformation false Inferred relationship Existential restriction modifier (core metadata concept) 1
Lymphangiomatosis Occurrence Congenital false Inferred relationship Existential restriction modifier (core metadata concept) 2
Lymphangiomatosis Associated morphology anomalie du développement false Inferred relationship Existential restriction modifier (core metadata concept) 2
Lymphangiomatosis Finding site Structure of lymphatic vessel false Inferred relationship Existential restriction modifier (core metadata concept) 2
Lymphangiomatosis Occurrence Congenital true Inferred relationship Existential restriction modifier (core metadata concept) 1
Lymphangiomatosis Associated morphology Lymphatic vessel tumour false Inferred relationship Existential restriction modifier (core metadata concept) 1
Lymphangiomatosis Finding site Structure of lymphatic vessel true Inferred relationship Existential restriction modifier (core metadata concept) 1
Lymphangiomatosis Pathological process (attribute) Pathological developmental process (qualifier value) true Inferred relationship Existential restriction modifier (core metadata concept) 1
Lymphangiomatosis Associated morphology Lymphangiomatosis true Inferred relationship Existential restriction modifier (core metadata concept) 1
Lymphangiomatosis Is a Angiomatosis true Inferred relationship Existential restriction modifier (core metadata concept)
Lymphangiomatosis Is a Mass of soft tissue true Inferred relationship Existential restriction modifier (core metadata concept)
Lymphangiomatosis Is a Lesion of soft tissue (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)
Lymphangiomatosis Is a Lymphatic malformation true Inferred relationship Existential restriction modifier (core metadata concept)

Inbound Relationships Type Active Source Characteristic Refinability Group
Segmental lymphangiomatosis (disorder) Is a False Lymphangiomatosis Inferred relationship Existential restriction modifier (core metadata concept)
Systemic lymphangiomatosis Is a False Lymphangiomatosis Inferred relationship Existential restriction modifier (core metadata concept)
Diffuse pulmonary lymphangiomatosis Is a True Lymphangiomatosis Inferred relationship Existential restriction modifier (core metadata concept)
A rare vascular anomaly or angioma characterised by multifocal malformed lymphatic channels lined by clusters or sheets of spindled lymphatic endothelial cells with a predilection for the thoracic cavity, but also involving extra-thoracic locations, especially bones and spleen. Typical clinical signs and symptoms are pericardial and pleural effusions, cough, dyspnoea, bleeding, and fractures secondary to bone involvement. Prognosis is generally poor due to the progressive nature of the condition. Is a True Lymphangiomatosis Inferred relationship Existential restriction modifier (core metadata concept)

This concept is not in any reference sets

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