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427213005: Autoimmune vasculitis (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2007. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
2662170019 Autoimmune vasculitis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
2675978018 Autoimmune vasculitis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
2662170019 Autoimmune vasculitis (disorder) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
2662170019 Autoimmune vasculitis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
2675978018 Autoimmune vasculitis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
2675978018 Autoimmune vasculitis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
224131000172112 vascularite auto-immune fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
224131000172112 vascularite auto-immune fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


18 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Autoimmune vasculitis (disorder) Is a Vasculitis (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)
Autoimmune vasculitis (disorder) Associated morphology inflammation false Inferred relationship Existential restriction modifier (core metadata concept) 1
Autoimmune vasculitis (disorder) Pathological process (attribute) Autoimmune process false Inferred relationship Existential restriction modifier (core metadata concept) 2
Autoimmune vasculitis (disorder) Finding site Blood vessel structure (body structure) false Inferred relationship Existential restriction modifier (core metadata concept) 1
Autoimmune vasculitis (disorder) Associated morphology inflammation false Inferred relationship Existential restriction modifier (core metadata concept) 1
Autoimmune vasculitis (disorder) Finding site Blood vessel structure (body structure) true Inferred relationship Existential restriction modifier (core metadata concept) 1
Autoimmune vasculitis (disorder) Is a Autoimmune disease true Inferred relationship Existential restriction modifier (core metadata concept)
Autoimmune vasculitis (disorder) Associated morphology Inflammatory morphology (morphologic abnormality) true Inferred relationship Existential restriction modifier (core metadata concept) 1
Autoimmune vasculitis (disorder) Pathological process (attribute) Autoimmune process true Inferred relationship Existential restriction modifier (core metadata concept) 1

Inbound Relationships Type Active Source Characteristic Refinability Group
Immunoglobulin A vasculitis Is a True Autoimmune vasculitis (disorder) Inferred relationship Existential restriction modifier (core metadata concept)
Systemic lupus erythematosus encephalitis Is a True Autoimmune vasculitis (disorder) Inferred relationship Existential restriction modifier (core metadata concept)
Rheumatoid vasculitis Is a True Autoimmune vasculitis (disorder) Inferred relationship Existential restriction modifier (core metadata concept)
Rheumatoid arteritis Is a False Autoimmune vasculitis (disorder) Inferred relationship Existential restriction modifier (core metadata concept)
Allergic granulomatosis angiitis (disorder) Is a True Autoimmune vasculitis (disorder) Inferred relationship Existential restriction modifier (core metadata concept)
STING-associated vasculopathy with onset in infancy Is a True Autoimmune vasculitis (disorder) Inferred relationship Existential restriction modifier (core metadata concept)
Microscopic polyangiitis (disorder) Is a True Autoimmune vasculitis (disorder) Inferred relationship Existential restriction modifier (core metadata concept)
Acute rheumatic fever with aortitis (disorder) Is a True Autoimmune vasculitis (disorder) Inferred relationship Existential restriction modifier (core metadata concept)
Immunoglobulin G4 related aortitis (disorder) Is a True Autoimmune vasculitis (disorder) Inferred relationship Existential restriction modifier (core metadata concept)
Vasculitis due to ADA2 deficiency is a rare, genetic, systemic and rheumatologic disease due to adenosine deaminase-2 inactivating mutations, combining variable features of autoinflammation, vasculitis, and a mild immunodeficiency. Variable clinical presentation includes chronic or recurrent systemic inflammation with fever, livedo reticularis or racemosa, early-onset ischemic or hemorrhagic strokes, peripheral neuropathy, abdominal pain, hepatosplenomegaly, portal hypertension, cutaneous polyarteritis nodosa, variable cytopenia and immunoglobulin deficiency. Is a True Autoimmune vasculitis (disorder) Inferred relationship Existential restriction modifier (core metadata concept)

This concept is not in any reference sets

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