Inbound Relationships |
Type |
Active |
Source |
Characteristic |
Refinability |
Group |
Pulmonary amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloidosis of skin |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid of cornea |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid of vitreous (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Laryngeal amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloidosis of spleen |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Hereditary cerebrovascular amyloidosis (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Localized hereditary amyloidosis (disorder) |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Familial lichen amyloidosis |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Papular cutaneous amyloid |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Poikilodermal cutaneous amyloid |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Localised non-hereditary amyloidosis |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Macular cutaneous amyloidosis |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Dominant primary localized cutaneous amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Localized amyloid deposit |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Gingival amyloidosis |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid of urinary bladder (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
AD type amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid of prostate |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid of testes |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid of ureter |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Cutaneous amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Familial amyloid nephropathy with urticaria AND deafness |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Bullous cutaneous amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Isolated atrial amyloid |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Isolated corneal amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Hereditary oculoleptomeningeal amyloid angiopathy (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Cerebrovascular amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Hereditary cerebral amyloid angiopathy, Icelandic type |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
3 |
Senile brain amyloidosis (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Amyloid nephropathy |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Hereditary cerebral amyloid angiopathy, Dutch type |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Localized amyloidosis |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Familial visceral amyloidosis, Ostertag type |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Ocular amyloid deposit |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Autonomic neuropathy due to amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Polyneuropathy due to amyloidosis (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Neuropathy in secondary amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Primary systemic (AL fibril type) amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid light chain amyloidosis due to multiple myeloma (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Primary systemic amyloidosis associated with occult plasma cell dyscrasia |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Macroglossia due to amyloidosis (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Pseudoscleroderma due to amyloid light-chain amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Secondary systemic amyloidosis affecting skin (AA fibril type) (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Hemodialysis-associated secondary amyloidosis of skin (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Heredofamilial systemic amyloidosis affecting skin (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Familial amyloid polyneuropathy with cutaneous amyloidosis (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Maculopapular amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Nodular amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Familial localized cutaneous amyloidosis (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Secondary localized cutaneous amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Systemic amyloidosis affecting skin (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloidosis limited to skin (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid corneal degeneration (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Amyloid light-chain nephropathy (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Amyloid A nephropathy (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
|
Cutaneous amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Hereditary cerebrovascular amyloidosis (disorder) |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Papular cutaneous amyloid |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid of urinary bladder (disorder) |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid of cornea |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloidosis limited to skin (disorder) |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Dominant primary localized cutaneous amyloidosis |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid of testes |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Laryngeal amyloidosis |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Familial localized cutaneous amyloidosis (disorder) |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid of prostate |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Familial amyloid polyneuropathy with cutaneous amyloidosis (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Maculopapular amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Secondary systemic amyloidosis affecting skin (AA fibril type) (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
AD type amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloidosis of skin |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Hereditary cerebral amyloid angiopathy, Dutch type |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Primary systemic amyloidosis associated with occult plasma cell dyscrasia |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Hemodialysis-associated secondary amyloidosis of skin (disorder) |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid light chain amyloidosis due to multiple myeloma (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Pseudoscleroderma due to amyloid light-chain amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Poikilodermal cutaneous amyloid |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Pulmonary amyloidosis |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid corneal degeneration (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Heredofamilial systemic amyloidosis affecting skin (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Secondary localized cutaneous amyloidosis |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Isolated corneal amyloidosis |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Bullous cutaneous amyloidosis |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Amyloid of vitreous (disorder) |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Primary systemic (AL fibril type) amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Nodular amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Systemic amyloidosis affecting skin (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Cerebrovascular amyloidosis |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Hereditary cerebral amyloid angiopathy, Icelandic type |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Hereditary cerebral amyloid angiopathy, Dutch type |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Primary localized cutaneous nodular amyloidosis |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Lichen amyloidosis is a rare chronic form of cutaneous amyloidosis, a skin disease characterized by the accumulation of amyloid deposits in the dermis, clinically characterized by the development of pruritic, often pigmented, hyperkeratotic papules on trunk and extremities, especially on the shins, and histologically by the deposition of amyloid or amyloid-like proteins in the papillary dermis. |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Hereditary cerebral hemorrhage with amyloidosis (disorder) |
Associated morphology |
False |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Primary localized cutaneous amyloidosis (disorder) |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
A rare primary cutaneous amyloidosis characterized by macular or reticulate hyperpigmentation with symmetrically distributed guttate hypo- and hyperpigmented lesions which progress gradually over the years to involve almost the entire body (with relative sparing of the face, hands, feet and neck). Patients are usually asymptomatic, however mild pruritus may be associated. Amyloid deposition in the papillary dermis is observed on skin biopsy. Systemic amyloidosis is not present and association with generalized morphea, atypical Parkinsonism, spasticity, motor weakness or colon carcinoma is rare. |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
AGel amyloidosis |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Lattice corneal dystrophy Type I |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Lattice corneal dystrophy |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
2 |
Amyloid of ureter |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |
Senile brain amyloidosis (disorder) |
Associated morphology |
True |
Focal amyloid |
Inferred relationship |
Existential restriction modifier (core metadata concept) |
1 |