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715863001: Autoimmune necrotizing myopathy (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2019. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3303966017 Autoimmune necrotizing myopathy (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3303967014 Autoimmune necrotizing myopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3303968016 Autoimmune necrotising myopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3303969012 Immune mediated necrotizing myopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3303970013 Immune mediated necrotising myopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5401142016 A rare form of idiopathic inflammatory myopathy characterized by acute or subacute, severe, symmetrical, proximal muscle weakness usually associated with muscle-specific antibodies (anti-HMGCR or anti-SRP). Histopathological characteristics include myocyte necrosis and regeneration without significant inflammation, and C5b-9 deposition on non-necrotic myofibers. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5401143014 A rare form of idiopathic inflammatory myopathy characterised by acute or subacute, severe, symmetrical, proximal muscle weakness usually associated with muscle-specific antibodies (anti-HMGCR or anti-SRP). Histopathological characteristics include myocyte necrosis and regeneration without significant inflammation, and C5b-9 deposition on non-necrotic myofibres. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3303966017 Autoimmune necrotizing myopathy (disorder) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
3303966017 Autoimmune necrotizing myopathy (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3303967014 Autoimmune necrotizing myopathy en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
3303967014 Autoimmune necrotizing myopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3303968016 Autoimmune necrotising myopathy en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
3303968016 Autoimmune necrotising myopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3303969012 Immune mediated necrotizing myopathy en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
3303969012 Immune mediated necrotizing myopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3303970013 Immune mediated necrotising myopathy en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
3303970013 Immune mediated necrotising myopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3303971012 A rare form of idiopathic inflammatory myopathy with clinical manifestation of acute or subacute proximal muscle weakness and histopathological features of myocyte necrosis and regeneration without significant inflammation. The main presenting feature is subacute severe symmetrical proximal myopathy with a markedly elevated creatine kinase level. The course is often severe but may be self-limiting and recovery may occur within weeks to months of discontinuing the causative agent, if identified. The disease is thought to be related to an immune response possibly triggered by drug therapy, connective tissue diseases, or cancer. The exact mechanism underling the disorder is not known but some autoantibodies appear to be a likely cause. Malignancy may be involved. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5401142016 A rare form of idiopathic inflammatory myopathy characterized by acute or subacute, severe, symmetrical, proximal muscle weakness usually associated with muscle-specific antibodies (anti-HMGCR or anti-SRP). Histopathological characteristics include myocyte necrosis and regeneration without significant inflammation, and C5b-9 deposition on non-necrotic myofibers. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5401143014 A rare form of idiopathic inflammatory myopathy characterised by acute or subacute, severe, symmetrical, proximal muscle weakness usually associated with muscle-specific antibodies (anti-HMGCR or anti-SRP). Histopathological characteristics include myocyte necrosis and regeneration without significant inflammation, and C5b-9 deposition on non-necrotic myofibres. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3430291001000117 Immunvermittelte nekrotisierende Myopathie de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
478891000172110 myopathie nécrosante auto-immune fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
478891000172110 myopathie nécrosante auto-immune fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3430291001000117 Immunvermittelte nekrotisierende Myopathie de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Autoimmune necrotizing myopathy Is a Autoimmune disease false Inferred relationship Existential restriction modifier (core metadata concept)
Autoimmune necrotizing myopathy Is a Inflammation of specific body organs false Inferred relationship Existential restriction modifier (core metadata concept)
Autoimmune necrotizing myopathy Is a Necrosis of anatomical site (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)
Autoimmune necrotizing myopathy Is a Idiopathic inflammatory myopathy (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)
Autoimmune necrotizing myopathy Associated morphology Necrotizing inflammation true Inferred relationship Existential restriction modifier (core metadata concept) 1
Autoimmune necrotizing myopathy Finding site Skeletal and/or smooth muscle structure (body structure) false Inferred relationship Existential restriction modifier (core metadata concept) 1
Autoimmune necrotizing myopathy Pathological process (attribute) Autoimmune process true Inferred relationship Existential restriction modifier (core metadata concept) 1
Autoimmune necrotizing myopathy Is a Autoimmune inflammation of skeletal muscle (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)
Autoimmune necrotizing myopathy Finding site Skeletal muscle structure true Inferred relationship Existential restriction modifier (core metadata concept) 1
Autoimmune necrotizing myopathy Is a Lesion of soft tissue (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
Autoimmune necrotizing myopathy Is a Injury of musculoskeletal system true Inferred relationship Existential restriction modifier (core metadata concept)
Autoimmune necrotizing myopathy Is a Injury of muscle true Inferred relationship Existential restriction modifier (core metadata concept)
Autoimmune necrotizing myopathy Is a Injury of soft tissue (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)
Autoimmune necrotizing myopathy Is a Lesion of skeletal muscle (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)

Inbound Relationships Type Active Source Characteristic Refinability Group

Reference Sets

Component annotation with string value reference set (foundation metadata concept)

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