Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2016. Module: SNOMED CT core
Descriptions:
Id | Description | Lang | Type | Status | Case? | Module |
3307260018 | Primary localized cutaneous nodular amyloidosis (disorder) | en | Fully specified name | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3307261019 | Primary localized cutaneous nodular amyloidosis | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3307262014 | Primary localised cutaneous nodular amyloidosis | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3307263016 | PLCNA - Primary localized cutaneous nodular amyloidosis | en | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
3307264010 | PLCNA - Primary localised cutaneous nodular amyloidosis | en | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
3872995015 | Nodular amyloidosis | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
5401376017 | Primary localized cutaneous nodular amyloidosis (PLCNA) is the most rare form of primary cutaneous amyloidosis, a skin disease characterized by the accumulation of amyloid deposits in the dermis, characterized clinically by yellowish waxy crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia and histologically by the localized deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. PLCNA can be associated with connective tissue disorders such as Sjögren's syndrome and CREST syndrome. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
5401377014 | Primary localised cutaneous nodular amyloidosis (PLCNA) is the most rare form of primary cutaneous amyloidosis, a skin disease characterised by the accumulation of amyloid deposits in the dermis, characterised clinically by yellowish waxy crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia and histologically by the localised deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. PLCNA can be associated with connective tissue disorders such as Sjögren's syndrome and CREST syndrome. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
3307260018 | Primary localized cutaneous nodular amyloidosis (disorder) | en | Fully specified name | Active | Only initial character case insensitive (core metadata concept) | SNOMED CT core |
3307260018 | Primary localized cutaneous nodular amyloidosis (disorder) | en | Fully specified name | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3307261019 | Primary localized cutaneous nodular amyloidosis | en | Synonym (core metadata concept) | Active | Only initial character case insensitive (core metadata concept) | SNOMED CT core |
3307261019 | Primary localized cutaneous nodular amyloidosis | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3307262014 | Primary localised cutaneous nodular amyloidosis | en | Synonym (core metadata concept) | Active | Only initial character case insensitive (core metadata concept) | SNOMED CT core |
3307262014 | Primary localised cutaneous nodular amyloidosis | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3307263016 | PLCNA - Primary localized cutaneous nodular amyloidosis | en | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
3307264010 | PLCNA - Primary localised cutaneous nodular amyloidosis | en | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
3872995015 | Nodular amyloidosis | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3307265011 | The most rare form of primary cutaneous amyloidosis, a skin disease characterized by the accumulation of amyloid deposits in the dermis. Clinical characteristics are yellowish waxy-crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia. Histological characteristics are the localized deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
3307266012 | The most rare form of primary cutaneous amyloidosis, a skin disease characterised by the accumulation of amyloid deposits in the dermis. Clinical characteristics are yellowish waxy-crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia. Histological characteristics are the localised deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
5401376017 | Primary localized cutaneous nodular amyloidosis (PLCNA) is the most rare form of primary cutaneous amyloidosis, a skin disease characterized by the accumulation of amyloid deposits in the dermis, characterized clinically by yellowish waxy crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia and histologically by the localized deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. PLCNA can be associated with connective tissue disorders such as Sjögren's syndrome and CREST syndrome. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
5401377014 | Primary localised cutaneous nodular amyloidosis (PLCNA) is the most rare form of primary cutaneous amyloidosis, a skin disease characterised by the accumulation of amyloid deposits in the dermis, characterised clinically by yellowish waxy crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia and histologically by the localised deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. PLCNA can be associated with connective tissue disorders such as Sjögren's syndrome and CREST syndrome. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
3449621001000111 | Noduläre kutane Amyloidose | de | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
6485111000241117 | amylose cutanée nodulaire primitive localisée | fr | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
6485121000241112 | ACNPL - amylose cutanée nodulaire primitive localisée | fr | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
6485131000241114 | amyloïdose cutanée nodulaire primitive localisée | fr | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
6485111000241117 | amylose cutanée nodulaire primitive localisée | fr | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
6485121000241112 | ACNPL - amylose cutanée nodulaire primitive localisée | fr | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
6485131000241114 | amyloïdose cutanée nodulaire primitive localisée | fr | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
3449621001000111 | Noduläre kutane Amyloidose | de | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
Outbound Relationships | Type | Target | Active | Characteristic | Refinability | Group | Values |
Primary localized cutaneous nodular amyloidosis | Is a | Nodular amyloidosis | false | Inferred relationship | Existential restriction modifier (core metadata concept) | ||
Primary localized cutaneous nodular amyloidosis | Associated morphology | Focal amyloid | true | Inferred relationship | Existential restriction modifier (core metadata concept) | 1 | |
Primary localized cutaneous nodular amyloidosis | Finding site | Skin structure | true | Inferred relationship | Existential restriction modifier (core metadata concept) | 1 | |
Primary localized cutaneous nodular amyloidosis | Is a | Primary localized cutaneous amyloidosis (disorder) | true | Inferred relationship | Existential restriction modifier (core metadata concept) |
Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group |
Reference Sets
Component annotation with string value reference set (foundation metadata concept)