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716704007: Primary localized cutaneous nodular amyloidosis (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2016. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3307260018 Primary localized cutaneous nodular amyloidosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3307261019 Primary localized cutaneous nodular amyloidosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3307262014 Primary localised cutaneous nodular amyloidosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3307263016 PLCNA - Primary localized cutaneous nodular amyloidosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3307264010 PLCNA - Primary localised cutaneous nodular amyloidosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3872995015 Nodular amyloidosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5401376017 Primary localized cutaneous nodular amyloidosis (PLCNA) is the most rare form of primary cutaneous amyloidosis, a skin disease characterized by the accumulation of amyloid deposits in the dermis, characterized clinically by yellowish waxy crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia and histologically by the localized deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. PLCNA can be associated with connective tissue disorders such as Sjögren's syndrome and CREST syndrome. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5401377014 Primary localised cutaneous nodular amyloidosis (PLCNA) is the most rare form of primary cutaneous amyloidosis, a skin disease characterised by the accumulation of amyloid deposits in the dermis, characterised clinically by yellowish waxy crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia and histologically by the localised deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. PLCNA can be associated with connective tissue disorders such as Sjögren's syndrome and CREST syndrome. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3307260018 Primary localized cutaneous nodular amyloidosis (disorder) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
3307260018 Primary localized cutaneous nodular amyloidosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3307261019 Primary localized cutaneous nodular amyloidosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
3307261019 Primary localized cutaneous nodular amyloidosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3307262014 Primary localised cutaneous nodular amyloidosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
3307262014 Primary localised cutaneous nodular amyloidosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3307263016 PLCNA - Primary localized cutaneous nodular amyloidosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3307264010 PLCNA - Primary localised cutaneous nodular amyloidosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3872995015 Nodular amyloidosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3307265011 The most rare form of primary cutaneous amyloidosis, a skin disease characterized by the accumulation of amyloid deposits in the dermis. Clinical characteristics are yellowish waxy-crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia. Histological characteristics are the localized deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3307266012 The most rare form of primary cutaneous amyloidosis, a skin disease characterised by the accumulation of amyloid deposits in the dermis. Clinical characteristics are yellowish waxy-crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia. Histological characteristics are the localised deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5401376017 Primary localized cutaneous nodular amyloidosis (PLCNA) is the most rare form of primary cutaneous amyloidosis, a skin disease characterized by the accumulation of amyloid deposits in the dermis, characterized clinically by yellowish waxy crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia and histologically by the localized deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. PLCNA can be associated with connective tissue disorders such as Sjögren's syndrome and CREST syndrome. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5401377014 Primary localised cutaneous nodular amyloidosis (PLCNA) is the most rare form of primary cutaneous amyloidosis, a skin disease characterised by the accumulation of amyloid deposits in the dermis, characterised clinically by yellowish waxy crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia and histologically by the localised deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. PLCNA can be associated with connective tissue disorders such as Sjögren's syndrome and CREST syndrome. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3449621001000111 Noduläre kutane Amyloidose de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6485111000241117 amylose cutanée nodulaire primitive localisée fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6485121000241112 ACNPL - amylose cutanée nodulaire primitive localisée fr Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6485131000241114 amyloïdose cutanée nodulaire primitive localisée fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6485111000241117 amylose cutanée nodulaire primitive localisée fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6485121000241112 ACNPL - amylose cutanée nodulaire primitive localisée fr Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6485131000241114 amyloïdose cutanée nodulaire primitive localisée fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3449621001000111 Noduläre kutane Amyloidose de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Primary localized cutaneous nodular amyloidosis Is a Nodular amyloidosis false Inferred relationship Existential restriction modifier (core metadata concept)
Primary localized cutaneous nodular amyloidosis Associated morphology Focal amyloid true Inferred relationship Existential restriction modifier (core metadata concept) 1
Primary localized cutaneous nodular amyloidosis Finding site Skin structure true Inferred relationship Existential restriction modifier (core metadata concept) 1
Primary localized cutaneous nodular amyloidosis Is a Primary localized cutaneous amyloidosis (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)

Inbound Relationships Type Active Source Characteristic Refinability Group

Reference Sets

Component annotation with string value reference set (foundation metadata concept)

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