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721226005: Hughes Stovin syndrome (disorder)

Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2017. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3324673014 Hughes Stovin syndrome (disorder) en Fully specified name Active Entire term case sensitive (core metadata concept) SNOMED CT core
3324676018 Hughes Stovin syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
5402650011 Hughes-Stovin syndrome (HSS) is a life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease. It is characterized by the association of multiple pulmonary artery aneurysms (PAAs) and peripheral venous thrombosis. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5402651010 Hughes-Stovin syndrome (HSS) is a life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease. It is characterised by the association of multiple pulmonary artery aneurysms (PAAs) and peripheral venous thrombosis. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3324673014 Hughes Stovin syndrome (disorder) en Fully specified name Active Entire term case sensitive (core metadata concept) SNOMED CT core
3324676018 Hughes Stovin syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3324678017 A life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease, with the association of multiple pulmonary artery aneurysms and peripheral venous thrombosis. Prevalence is unknown but fewer than 30 cases have been reported in the literature since its first description in 1959 by Hughes and Stovin. Patients (mostly men aged 12-40 years) generally present with the nonspecific signs of pulmonary artery aneurysms, following a history of peripheral venous thrombosis. Other associated signs may include fever and intracranial hypertension. Aneurysms can occur anywhere in the systemic circulation. Recurrent phlebitis also commonly involves the large vessels, resulting in thrombus formation. In general, there is a predisposition for thrombus formation affecting the peripheral veins. It is assumed the disease is a form of vasculitis following a similar mechanism of pathogenesis to that thought to be involved in Behcet disease. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5402650011 Hughes-Stovin syndrome (HSS) is a life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease. It is characterized by the association of multiple pulmonary artery aneurysms (PAAs) and peripheral venous thrombosis. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5402651010 Hughes-Stovin syndrome (HSS) is a life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behcet disease. It is characterised by the association of multiple pulmonary artery aneurysms (PAAs) and peripheral venous thrombosis. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3451391001000116 Hughes-Stovin-Syndrom de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
5481841000241110 syndrome de Hughes Stovin fr Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
5481841000241110 syndrome de Hughes Stovin fr Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3451391001000116 Hughes-Stovin-Syndrom de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module

0 descendants.

Expanded Value Set

Outbound Relationships Type Target Active Characteristic Refinability Group Values
Hughes Stovin syndrome (disorder) Associated morphology inflammation false Inferred relationship Existential restriction modifier (core metadata concept) 1
Hughes Stovin syndrome (disorder) Finding site Systemic vascular structure true Inferred relationship Existential restriction modifier (core metadata concept) 1
Hughes Stovin syndrome (disorder) Is a Vasculitis (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
Hughes Stovin syndrome (disorder) Associated morphology Inflammatory morphology (morphologic abnormality) true Inferred relationship Existential restriction modifier (core metadata concept) 1
Hughes Stovin syndrome (disorder) Is a Inflammation of systemic vasculature (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)
Inbound Relationships Type Active Source Characteristic Refinability Group

Reference Sets

Component annotation with string value reference set (foundation metadata concept)

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