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737582007: Hemiparkinsonism hemiatrophy syndrome (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 30-Sep 2021. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3528395016 Hemiparkinsonism hemiatrophy syndrome (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3528396015 Hemiparkinsonism hemiatrophy syndrome en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5403906018 Hemiparkinsonism-hemiatrophy syndrome is a rare parkinsonian disorder characterized by unilateral body atrophy and slowly progressive, ipsilateral, hemiparkinsonian signs (bradykinesia, rigidity, and tremor). Patients typically present with unilateral, action-induced dystonia, in upper or lower limbs, that progresses and becomes bilateral or with tremor which occurs predominantly at rest and progresses to hemiparkinsonism. Scoliosis, scapular winging, raised shoulders, brisk reflexes and extensor plantar responses are frequently associated. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5403907010 Hemiparkinsonism-hemiatrophy syndrome is a rare parkinsonian disorder characterised by unilateral body atrophy and slowly progressive, ipsilateral, hemiparkinsonian signs (bradykinesia, rigidity, and tremor). Patients typically present with unilateral, action-induced dystonia, in upper or lower limbs, that progresses and becomes bilateral or with tremor which occurs predominantly at rest and progresses to hemiparkinsonism. Scoliosis, scapular winging, raised shoulders, brisk reflexes and extensor plantar responses are frequently associated. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3528395016 Hemiparkinsonism hemiatrophy syndrome (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3528396015 Hemiparkinsonism hemiatrophy syndrome en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3528397012 A rare parkinsonian disorder with characteristics of unilateral body atrophy and slowly progressive, ipsilateral hemiparkinsonian signs (bradykinesia, rigidity, and tremor). Patients typically present with unilateral, action-induced dystonia, in upper or lower limbs, that progresses and becomes bilateral or with tremor which occurs predominantly at rest and progresses to hemiparkinsonism. Scoliosis, scapular winging, raised shoulders, brisk reflexes and extensor plantars are frequently associated. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5403906018 Hemiparkinsonism-hemiatrophy syndrome is a rare parkinsonian disorder characterized by unilateral body atrophy and slowly progressive, ipsilateral, hemiparkinsonian signs (bradykinesia, rigidity, and tremor). Patients typically present with unilateral, action-induced dystonia, in upper or lower limbs, that progresses and becomes bilateral or with tremor which occurs predominantly at rest and progresses to hemiparkinsonism. Scoliosis, scapular winging, raised shoulders, brisk reflexes and extensor plantar responses are frequently associated. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5403907010 Hemiparkinsonism-hemiatrophy syndrome is a rare parkinsonian disorder characterised by unilateral body atrophy and slowly progressive, ipsilateral, hemiparkinsonian signs (bradykinesia, rigidity, and tremor). Patients typically present with unilateral, action-induced dystonia, in upper or lower limbs, that progresses and becomes bilateral or with tremor which occurs predominantly at rest and progresses to hemiparkinsonism. Scoliosis, scapular winging, raised shoulders, brisk reflexes and extensor plantar responses are frequently associated. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3440111001000115 Hemiparkinson-Hemiatrophie-Syndrom de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6276861000241113 syndrome d'hémiparkinsonisme et hémiatrophie fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6276871000241117 syndrome HP-HA (hémiparkinsonisme-hémiatrophie) fr Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6276861000241113 syndrome d'hémiparkinsonisme et hémiatrophie fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6276871000241117 syndrome HP-HA (hémiparkinsonisme-hémiatrophie) fr Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3440111001000115 Hemiparkinson-Hemiatrophie-Syndrom de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Hemiparkinsonism hemiatrophy syndrome (disorder) Is a Parkinsonism true Inferred relationship Existential restriction modifier (core metadata concept)
Hemiparkinsonism hemiatrophy syndrome (disorder) Is a Degenerative disorder true Inferred relationship Existential restriction modifier (core metadata concept)
Hemiparkinsonism hemiatrophy syndrome (disorder) Finding site Basal ganglion structure (body structure) true Inferred relationship Existential restriction modifier (core metadata concept) 1
Hemiparkinsonism hemiatrophy syndrome (disorder) Associated morphology Hemiatrophy (morphologic abnormality) true Inferred relationship Existential restriction modifier (core metadata concept) 2
Hemiparkinsonism hemiatrophy syndrome (disorder) Finding site Structure of half of body lateral to midsagittal plane true Inferred relationship Existential restriction modifier (core metadata concept) 2
Hemiparkinsonism hemiatrophy syndrome (disorder) Interprets Movement true Inferred relationship Existential restriction modifier (core metadata concept) 4
Hemiparkinsonism hemiatrophy syndrome (disorder) Has interpretation Slow true Inferred relationship Existential restriction modifier (core metadata concept) 4

Inbound Relationships Type Active Source Characteristic Refinability Group

Reference Sets

Component annotation with string value reference set (foundation metadata concept)

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