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761958009: Malignant peripheral nerve sheath neoplasm with perineurial differentiation (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2018. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3634392015 Malignant peripheral nerve sheath tumour with perineurial differentiation en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634393013 Malignant peripheral nerve sheath neoplasm with perineurial differentiation en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634394019 Malignant peripheral nerve sheath tumor with perineurial differentiation en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634395018 Malignant peripheral nerve sheath neoplasm with perineurial differentiation (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634396017 Malignant perineurioma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634392015 Malignant peripheral nerve sheath tumour with perineurial differentiation en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634393013 Malignant peripheral nerve sheath neoplasm with perineurial differentiation en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634394019 Malignant peripheral nerve sheath tumor with perineurial differentiation en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634395018 Malignant peripheral nerve sheath neoplasm with perineurial differentiation (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634396017 Malignant perineurioma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3634399012 A rare soft tissue sarcoma composed predominantly of spindle-shaped neoplastic cells showing perineurial differentiation and displaying abundant cellular pleomorphism or anaplasia, frequent mitoses, tumour necrosis and high metastatic potential. It often presents as a soft, painless, solid mass in subcutaneous tissues of the trunk or limbs, but tumours have also been described in the facial area, mediastinum, retroperitoneum, pancreas, paravertebral column and the pelvic soft tissues. Frequent local recurrence and distant metastatic spread has been reported. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3634400017 A rare soft tissue sarcoma composed predominantly of spindle-shaped neoplastic cells showing perineurial differentiation and displaying abundant cellular pleomorphism or anaplasia, frequent mitoses, tumor necrosis and high metastatic potential. It often presents as a soft, painless, solid mass in subcutaneous tissues of the trunk or limbs, but tumors have also been described in the facial area, mediastinum, retroperitoneum, pancreas, paravertebral column and the pelvic soft tissues. Frequent local recurrence and distant metastatic spread has been reported. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3431251001000115 Nervenscheidentumor, maligner peripherer, mit perineurialer Differenzierung de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6336731000241118 néoplasme malin d'une gaine nerveuse périphérique avec différenciation périneurale fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6336741000241111 tumeur maligne de la gaine d'un nerf périphérique avec différenciation périneurale fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6336731000241118 néoplasme malin d'une gaine nerveuse périphérique avec différenciation périneurale fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
6336741000241111 tumeur maligne de la gaine d'un nerf périphérique avec différenciation périneurale fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3431251001000115 Nervenscheidentumor, maligner peripherer, mit perineurialer Differenzierung de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


1 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Malignant peripheral nerve sheath tumor with perineurial differentiation Associated morphology Perineurioma, malignant true Inferred relationship Existential restriction modifier (core metadata concept) 1
Malignant peripheral nerve sheath tumor with perineurial differentiation Is a Malignant peripheral nerve sheath tumor (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)

Inbound Relationships Type Active Source Characteristic Refinability Group
Primary malignant peripheral nerve sheath tumour with perineurial differentiation Is a True Malignant peripheral nerve sheath tumor with perineurial differentiation Inferred relationship Existential restriction modifier (core metadata concept)

This concept is not in any reference sets

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