Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2018. Module: SNOMED CT core
Descriptions:
Id | Description | Lang | Type | Status | Case? | Module |
3634392015 | Malignant peripheral nerve sheath tumour with perineurial differentiation | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3634393013 | Malignant peripheral nerve sheath neoplasm with perineurial differentiation | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3634394019 | Malignant peripheral nerve sheath tumor with perineurial differentiation | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3634395018 | Malignant peripheral nerve sheath neoplasm with perineurial differentiation (disorder) | en | Fully specified name | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3634396017 | Malignant perineurioma | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3634392015 | Malignant peripheral nerve sheath tumour with perineurial differentiation | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3634393013 | Malignant peripheral nerve sheath neoplasm with perineurial differentiation | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3634394019 | Malignant peripheral nerve sheath tumor with perineurial differentiation | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3634395018 | Malignant peripheral nerve sheath neoplasm with perineurial differentiation (disorder) | en | Fully specified name | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3634396017 | Malignant perineurioma | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
3634399012 | A rare soft tissue sarcoma composed predominantly of spindle-shaped neoplastic cells showing perineurial differentiation and displaying abundant cellular pleomorphism or anaplasia, frequent mitoses, tumour necrosis and high metastatic potential. It often presents as a soft, painless, solid mass in subcutaneous tissues of the trunk or limbs, but tumours have also been described in the facial area, mediastinum, retroperitoneum, pancreas, paravertebral column and the pelvic soft tissues. Frequent local recurrence and distant metastatic spread has been reported. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
3634400017 | A rare soft tissue sarcoma composed predominantly of spindle-shaped neoplastic cells showing perineurial differentiation and displaying abundant cellular pleomorphism or anaplasia, frequent mitoses, tumor necrosis and high metastatic potential. It often presents as a soft, painless, solid mass in subcutaneous tissues of the trunk or limbs, but tumors have also been described in the facial area, mediastinum, retroperitoneum, pancreas, paravertebral column and the pelvic soft tissues. Frequent local recurrence and distant metastatic spread has been reported. | en | Definition | Active | Entire term case sensitive (core metadata concept) | SNOMED CT core |
3431251001000115 | Nervenscheidentumor, maligner peripherer, mit perineurialer Differenzierung | de | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
6336731000241118 | néoplasme malin d'une gaine nerveuse périphérique avec différenciation périneurale | fr | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
6336741000241111 | tumeur maligne de la gaine d'un nerf périphérique avec différenciation périneurale | fr | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
6336731000241118 | néoplasme malin d'une gaine nerveuse périphérique avec différenciation périneurale | fr | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
6336741000241111 | tumeur maligne de la gaine d'un nerf périphérique avec différenciation périneurale | fr | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
3431251001000115 | Nervenscheidentumor, maligner peripherer, mit perineurialer Differenzierung | de | Synonym (core metadata concept) | Active | Entire term case sensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
Outbound Relationships | Type | Target | Active | Characteristic | Refinability | Group | Values |
Malignant peripheral nerve sheath tumor with perineurial differentiation | Associated morphology | Perineurioma, malignant | true | Inferred relationship | Existential restriction modifier (core metadata concept) | 1 | |
Malignant peripheral nerve sheath tumor with perineurial differentiation | Is a | Malignant peripheral nerve sheath tumor (disorder) | true | Inferred relationship | Existential restriction modifier (core metadata concept) |
Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group |
Primary malignant peripheral nerve sheath tumour with perineurial differentiation | Is a | True | Malignant peripheral nerve sheath tumor with perineurial differentiation | Inferred relationship | Existential restriction modifier (core metadata concept) |
This concept is not in any reference sets