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770402000: Aleukemic mast cell leukemia (disorder)


    Status: retired, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Mar 2023. Module: SNOMED CT core

    Descriptions:

    Id Description Lang Type Status Case? Module
    3700697011 Aleukemic mast cell leukemia en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    3700698018 Aleukemic mast cell leukemia (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
    3700699014 Aleukaemic mast cell leukaemia en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    3700697011 Aleukemic mast cell leukemia en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    3700698018 Aleukemic mast cell leukemia (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
    3700699014 Aleukaemic mast cell leukaemia en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
    3700700010 A very rare aggressive form of systemic mastocytosis characterised by abnormal growth and proliferation of neoplastic mast cells in the bone marrow and/or blood, as well as other tissues such as the liver, peritoneum, spleen or bones. Patients typically present with symptoms related to mast cell activation (for example hot flushes, fever, malaise, diarrhoea, tachycardia), weight loss, anorexia, hepatosplenomegaly or less frequently cutaneous mastocytosis. Gastroduodenal ulcers (often complicated by haemorrhage), ascites and portal hypertension have also been reported. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
    3700701014 A very rare aggressive form of systemic mastocytosis characterized by abnormal growth and proliferation of neoplastic mast cells in the bone marrow and/or blood, as well as other tissues such as the liver, peritoneum, spleen or bones. Patients typically present with symptoms related to mast cell activation (for example hot flushes, fever, malaise, diarrhea, tachycardia), weight loss, anorexia, hepatosplenomegaly or less frequently cutaneous mastocytosis. Gastroduodenal ulcers (often complicated by hemorrhage), ascites and portal hypertension have also been reported. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
    986131000172111 leucémie mastocytaire aleucémique fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
    986131000172111 leucémie mastocytaire aleucémique fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


    0 descendants.

    Expanded Value Set


    Outbound Relationships Type Target Active Characteristic Refinability Group Values
    leucémie mastocytaire aleucémique Finding site Hematopoietic system structure false Inferred relationship Existential restriction modifier (core metadata concept) 1
    leucémie mastocytaire aleucémique Is a Systemic mast cell disease (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
    leucémie mastocytaire aleucémique Is a Mast cell leukemia (clinical) false Inferred relationship Existential restriction modifier (core metadata concept)
    leucémie mastocytaire aleucémique Associated morphology Mast cell leukaemia false Inferred relationship Existential restriction modifier (core metadata concept) 1
    leucémie mastocytaire aleucémique Pathological process (attribute) Abnormal immune process (qualifier value) false Inferred relationship Existential restriction modifier (core metadata concept) 2
    leucémie mastocytaire aleucémique Is a Leukemia, disease (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
    leucémie mastocytaire aleucémique Is a Mast cell neoplasm false Inferred relationship Existential restriction modifier (core metadata concept)
    leucémie mastocytaire aleucémique Associated morphology Hyperplasia false Inferred relationship Existential restriction modifier (core metadata concept) 3
    leucémie mastocytaire aleucémique Is a Malignant white blood cell disorder false Inferred relationship Existential restriction modifier (core metadata concept)
    leucémie mastocytaire aleucémique Finding site Mast cell false Inferred relationship Existential restriction modifier (core metadata concept) 3
    leucémie mastocytaire aleucémique Is a Aleukemic leukemia false Inferred relationship Existential restriction modifier (core metadata concept)
    leucémie mastocytaire aleucémique Pathological process (attribute) Abnormal immune process (qualifier value) false Inferred relationship Existential restriction modifier (core metadata concept) 2
    leucémie mastocytaire aleucémique Associated morphology Hyperplasia false Inferred relationship Existential restriction modifier (core metadata concept) 2
    leucémie mastocytaire aleucémique Finding site Mast cell false Inferred relationship Existential restriction modifier (core metadata concept) 2
    leucémie mastocytaire aleucémique Finding site Hematopoietic system structure false Inferred relationship Existential restriction modifier (core metadata concept) 2
    leucémie mastocytaire aleucémique Associated morphology Leukemia false Inferred relationship Existential restriction modifier (core metadata concept) 2

    Inbound Relationships Type Active Source Characteristic Refinability Group

    Reference Sets

    Concept inactivation indicator attribute value reference set (foundation metadata concept)

    REPLACED BY association reference set (foundation metadata concept)

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