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773691007: Congenital erosive and vesicular dermatosis (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2019. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3725796017 Congenital erosive and vesicular dermatosis with reticulated supple scarring en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3725797014 Congenital erosive and vesicular dermatosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3725798016 CEVD - congenital erosive and vesicular dermatosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3725799012 Congenital erosive and vesicular dermatosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3725800011 A rare idiopathic skin disease with characteristics of widespread, congenital, superficial erosions and vesicles (often involving more than 75% of the body) which heal leaving scars with a supple, symmetrical, reticulated pattern, frequently resulting in cicatricial alopecia and hyperthermia and/or hypohidrosis. Nail anomalies, neurodevelopmental and ophthalmologic abnormalities, tongue atrophy and preterm birth, with or without history of chorioamnionitis, are commonly associated. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3725796017 Congenital erosive and vesicular dermatosis with reticulated supple scarring en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3725797014 Congenital erosive and vesicular dermatosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3725798016 CEVD - congenital erosive and vesicular dermatosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3725799012 Congenital erosive and vesicular dermatosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3725800011 A rare idiopathic skin disease with characteristics of widespread, congenital, superficial erosions and vesicles (often involving more than 75% of the body) which heal leaving scars with a supple, symmetrical, reticulated pattern, frequently resulting in cicatricial alopecia and hyperthermia and/or hypohidrosis. Nail anomalies, neurodevelopmental and ophthalmologic abnormalities, tongue atrophy and preterm birth, with or without history of chorioamnionitis, are commonly associated. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
3437941001000116 Dermatose, erosive und vesikuläre, kongenital de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
953831000172115 dermatose érosive et vésiculeuse congénitale avec cicatrices réticulées fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
994411000172119 dermatose érosive et vésiculaire congénitale fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
953831000172115 dermatose érosive et vésiculeuse congénitale avec cicatrices réticulées fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
994411000172119 dermatose érosive et vésiculaire congénitale fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3437941001000116 Dermatose, erosive und vesikuläre, kongenital de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Congenital erosive and vesicular dermatosis (disorder) Is a Idiopathic disease true Inferred relationship Existential restriction modifier (core metadata concept)
Congenital erosive and vesicular dermatosis (disorder) Occurrence Congenital true Inferred relationship Existential restriction modifier (core metadata concept) 1
Congenital erosive and vesicular dermatosis (disorder) Pathological process (attribute) Pathological developmental process (qualifier value) true Inferred relationship Existential restriction modifier (core metadata concept) 1
Congenital erosive and vesicular dermatosis (disorder) Occurrence Congenital true Inferred relationship Existential restriction modifier (core metadata concept) 2
Congenital erosive and vesicular dermatosis (disorder) Associated morphology Vesicular inflammation true Inferred relationship Existential restriction modifier (core metadata concept) 2
Congenital erosive and vesicular dermatosis (disorder) Is a Skin ulcer (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)
Congenital erosive and vesicular dermatosis (disorder) Pathological process (attribute) Pathological developmental process (qualifier value) true Inferred relationship Existential restriction modifier (core metadata concept) 2
Congenital erosive and vesicular dermatosis (disorder) Associated morphology Ulcerative inflammation true Inferred relationship Existential restriction modifier (core metadata concept) 1
Congenital erosive and vesicular dermatosis (disorder) Is a Congenital anomaly of skin (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)
Congenital erosive and vesicular dermatosis (disorder) Finding site Skin structure true Inferred relationship Existential restriction modifier (core metadata concept) 2
Congenital erosive and vesicular dermatosis (disorder) Is a Inflammatory dermatosis (disorder) true Inferred relationship Existential restriction modifier (core metadata concept)
Congenital erosive and vesicular dermatosis (disorder) Finding site Skin structure true Inferred relationship Existential restriction modifier (core metadata concept) 1
Congenital erosive and vesicular dermatosis (disorder) Is a Inflammation of specific body organs false Inferred relationship Existential restriction modifier (core metadata concept)
Congenital erosive and vesicular dermatosis (disorder) Is a Vesicle of skin true Inferred relationship Existential restriction modifier (core metadata concept)

Inbound Relationships Type Active Source Characteristic Refinability Group

This concept is not in any reference sets

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