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89155008: Systemic sclerosis (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2019. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
147833014 Systemic sclerosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
201443013 Systemic scleroderma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
508372014 Thibierge-Weissenbach syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
508375011 SS - Systemic sclerosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
831989015 Systemic sclerosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
147833014 Systemic sclerosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
147833014 Systemic sclerosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
147834015 Progressive systemic sclerosis en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
147835019 Scleroderma en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
201443013 Systemic scleroderma en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
201443013 Systemic scleroderma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
508372014 Thibierge-Weissenbach syndrome en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
508373016 PSS - Progressive systemic sclerosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
508374010 Scleroderma syndrome en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
508374010 Scleroderma syndrome en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
508375011 SS - Systemic sclerosis en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
831989015 Systemic sclerosis (disorder) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
831989015 Systemic sclerosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
1043941000195118 sclerosi sistemica it Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3454461001000115 Systemische Sklerodermie de Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
30031000188113 sclérodermie fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
248661000172118 sclérose systémique fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
1008431000241115 sclérodermie systémique fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
1008591000241118 sclérodermie généralisée fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
30031000188113 sclérodermie fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
248661000172118 sclérose systémique fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
1008431000241115 sclérodermie systémique fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
1008591000241118 sclérodermie généralisée fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
1043941000195118 sclerosi sistemica it Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3454461001000115 Systemische Sklerodermie de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3454461001000115 Systemische Sklerodermie de Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3454471001000112 Sklerodermie de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


17 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Systemic sclerosis Is a Disorder of fascia false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Is a Multisystem disorder S-T false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Is a Disorder of integument false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Is a Collagen disease false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Finding site Structure of skin region (body structure) false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Associated morphology Sclerosis (morphologic abnormality) false Inferred relationship Existential restriction modifier (core metadata concept) 1
Systemic sclerosis Finding site Connective tissue false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Finding site Connective tissue structure (body structure) false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Finding site Structure of fascia (body structure) false Inferred relationship Existential restriction modifier (core metadata concept) 1
Systemic sclerosis Is a Disorder of skin (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Is a trouble multisytémique false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Is a sclérodermie false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Finding site Structure of collagen fibers of skin false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Is a Lesion of soft tissue (disorder) false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Has definitional manifestation Immune system finding false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Pathological process (attribute) Autoimmune process false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Associated morphology Sclerosis (morphologic abnormality) false Inferred relationship Existential restriction modifier (core metadata concept) 1
Systemic sclerosis Finding site Structure of fascia (body structure) false Inferred relationship Existential restriction modifier (core metadata concept) 1
Systemic sclerosis Is a Autoimmune disease false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Associated morphology Fibrosis (morphologic abnormality) false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Associated morphology Fibrosis (morphologic abnormality) true Inferred relationship Existential restriction modifier (core metadata concept) 1
Systemic sclerosis Is a Systemic disease true Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Finding site Connective tissue structure (body structure) true Inferred relationship Existential restriction modifier (core metadata concept) 1
Systemic sclerosis Pathological process (attribute) Autoimmune process true Inferred relationship Existential restriction modifier (core metadata concept) 1
Systemic sclerosis Is a Autoimmune connective tissue disorder false Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis Is a A rare autoimmune connective tissue disorder characterized by abnormal hardening of the skin and sometimes other organs. It is classified into two main forms: localized scleroderma and systemic sclerosis (SSc), the latter comprising three subsets; diffuse cutaneous SSc (dcSSc), limited cutaneous SSc (lcSSc) and limited SSc (lSSc). Localized scleroderma is the cutaneous form of scleroderma characterized by fibrosis of the skin causing cutaneous plaques (morphea) or strips (linear scleroderma). Systemic sclerosis (SSc) is a generalized disorder characterized by fibrosis and vascular obliteration in the skin and organs, particularly, lungs, heart, and digestive tract. The exact cause of scleroderma is unknown. The disease originates from an autoimmune reaction, which leads to localized overproduction of collagen. In some cases, the condition is associated with exposure to chemicals. Other suggested causes include genetic and infectious mechanisms. true Inferred relationship Existential restriction modifier (core metadata concept)

Inbound Relationships Type Active Source Characteristic Refinability Group
Pseudoatrophoderma colli Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
sclérodermie avec atteinte organique ou systémique Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
sclérodermie avec atteinte multisystémique Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Juvenile scleroderma Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Scleroderma variant Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis with limited cutaneous involvement Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Limited systemic sclerosis Is a True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis, diffuse Is a True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Systemic sclerosis sine scleroderma Is a True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Linear scleroderma Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Dilated cardiomyopathy due to systemic sclerosis (disorder) Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Pericarditis due to systemic sclerosis Is a True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
sclérose systémique due à des médicaments et des produits chimiques Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Cold flexed fingers Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
[X]Other forms of systemic sclerosis Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Scleroderma NOS Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Lung disease with systemic sclerosis Associated finding False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Lung disease with systemic sclerosis Is a True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Occupational scleroderma Is a True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Cutaneous complication of systemic sclerosis (disorder) Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Scleroderma in newborn Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Family history: Scleroderma Associated finding False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 1
Cutaneous complication of systemic sclerosis (disorder) Associated with True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 1
Scleroderma-associated calcinosis (disorder) Associated with False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Scleroderma-associated hypermelanosis (disorder) Associated with False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Scleroderma-associated telangiectasia (disorder) Associated with False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Scleroderma-associated nailfold telangiectasia (disorder) Associated with False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Scleroderma-associated necrotizing vasculitis (disorder) Associated with True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Poikiloderma due to scleroderma Associated with False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Scleroderma-associated nail dystrophy (disorder) Associated with True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 4
Family history: Scleroderma Associated finding False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 1
Progressive systemic sclerosis (disorder) Is a True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Hypothyroidism due to scleroderma Due to False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Myopathy due to scleroderma Associated with False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 1
Dilated cardiomyopathy due to systemic sclerosis (disorder) Due to False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Pericarditis due to systemic sclerosis Due to True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 3
Family history of systemic sclerosis (situation) Associated finding False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 1
Family history of systemic sclerosis (situation) Associated finding True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 1
Dilated cardiomyopathy due to systemic sclerosis (disorder) Associated with False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Polyneuropathy due to systemic sclerosis Due to True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 1
Reynolds syndrome (RS) is an autoimmune disorder characterised by the association of primary biliary cirrhosis (PBC) with limited cutaneous systemic sclerosis (lcSSc). Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Glomerulonephritis co-occurrent and due to scleroderma (disorder) Due to False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Pediatric onset systemic sclerosis (disorder) Is a True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Neonatal scleroderma Is a False Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Renal involvement in scleroderma (disorder) Is a True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)
Scleroderma-associated calcinosis (disorder) Due to True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Scleroderma-associated hypermelanosis (disorder) Due to True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Scleroderma-associated telangiectasia (disorder) Due to True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Scleroderma-associated nailfold telangiectasia (disorder) Due to True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Dilated cardiomyopathy due to systemic sclerosis (disorder) Due to True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Gingival disease due to systemic sclerosis Due to True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Disorder of skeletal muscle due to systemic sclerosis (disorder) Due to True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Hypothyroidism due to systemic sclerosis (disorder) Due to True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept) 2
Systemic sclerosis caused by chemical (disorder) Is a True Systemic sclerosis Inferred relationship Existential restriction modifier (core metadata concept)

This concept is not in any reference sets

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