FHIR © HL7.org  |  Server Home  |  FHIR Server FHIR Server 3.7.4-SNAPSHOT  |  FHIR Version n/a  User: [n/a]

733627006: Primary cutaneous gamma-delta-positive T-cell lymphoma (disorder)

Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2020. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3474593010 Primary cutaneous gamma-delta-positive T-cell lymphoma (disorder) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
3474594016 Primary cutaneous gamma-delta-positive T-cell lymphoma en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
3784476010 Primary cutaneous gamma-delta T-cell lymphoma en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core
5403841015 Primary cutaneous gamma/delta-positive T-cell lymphoma is a rare, usually aggressive, subtype of cutaneous T-cell lymphoma characterized by infiltration of the epidermis, dermis or subcutaneous tissue by a clonal population of mature, gamma/delta positive cytotoxic T-cells. Typically it presents with ulcerating plaques, tumors, or subcutaneous nodules on the skin of the extremities, however, frequent involvement of mucosal and extranodal sites (such as the nasal cavity, gastrointestinal tract or lungs) is also observed. Cases associated with panniculitis may present with hemophagocytic syndrome (abrupt onset of fever, rash, cytopenia, hepatosplenomegaly and neurological compromise). Infiltration of lymph nodes, spleen and bone marrow is uncommon and resistance to multilineage chemotherapy is reported. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core
5403842010 Primary cutaneous gamma/delta-positive T-cell lymphoma is a rare, usually aggressive, subtype of cutaneous T-cell lymphoma characterised by infiltration of the epidermis, dermis or subcutaneous tissue by a clonal population of mature, gamma/delta positive cytotoxic T-cells. Typically it presents with ulcerating plaques, tumours, or subcutaneous nodules on the skin of the extremities, however, frequent involvement of mucosal and extranodal sites (such as the nasal cavity, gastrointestinal tract or lungs) is also observed. Cases associated with panniculitis may present with haemophagocytic syndrome (abrupt onset of fever, rash, cytopenia, hepatosplenomegaly and neurological compromise). Infiltration of lymph nodes, spleen and bone marrow is uncommon and resistance to multilineage chemotherapy is reported. en Definition Active Entire term case sensitive (core metadata concept) SNOMED CT core

0 descendants.

Expanded Value Set

Outbound Relationships Type Target Active Characteristic Refinability Group Values
Primary cutaneous gamma-delta-positive T-cell lymphoma (disorder) Is a Primary cutaneous T-cell lymphoma (disorder) true Inferred relationship Some
Primary cutaneous gamma-delta-positive T-cell lymphoma (disorder) Associated morphology Primary cutaneous gamma-delta T-cell lymphoma (morphologic abnormality) true Inferred relationship Some 1
Primary cutaneous gamma-delta-positive T-cell lymphoma (disorder) Finding site Skin structure true Inferred relationship Some 1
Inbound Relationships Type Active Source Characteristic Refinability Group

Reference Sets

Component annotation with string value reference set (foundation metadata concept)

Back to Start