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111318005: Congenital cystic adenomatoid malformation of lung (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2002. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
178550012 Congenital cystic adenomatoid malformation of lung en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
630279015 Congenital cystic adenomatoid malformation of lung (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
1219630019 Congenital cystic adenomatoid malformation of the lung en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3533619010 CPAM - Congenital pulmonary airway malformation en Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT core
3533620016 Congenital pulmonary airway malformation en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
4750151000241116 malformation adénomatoïde kystique du poumon fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3454801001000118 Kongenitale Fehlbildung der Atemwege de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


5 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Congenital cystic adenomatoid malformation of lung (disorder) Is a Congenital cystic lung false Inferred relationship Some
Congenital cystic adenomatoid malformation of lung (disorder) Occurrence Congenital false Inferred relationship Some
Congenital cystic adenomatoid malformation of lung (disorder) Finding site Lung structure true Inferred relationship Some 1
Congenital cystic adenomatoid malformation of lung (disorder) Associated morphology Congenital cavitation false Inferred relationship Some 1
Congenital cystic adenomatoid malformation of lung (disorder) Associated morphology Fibrocysticystic change (morphologic abnormality) false Inferred relationship Some
Congenital cystic adenomatoid malformation of lung (disorder) Is a Congenital anomaly of trunk false Inferred relationship Some
Congenital cystic adenomatoid malformation of lung (disorder) Associated morphology Congenital cavitation false Inferred relationship Some 1
Congenital cystic adenomatoid malformation of lung (disorder) Finding site Lung structure false Inferred relationship Some 1
Congenital cystic adenomatoid malformation of lung (disorder) Occurrence Congenital false Inferred relationship Some 2
Congenital cystic adenomatoid malformation of lung (disorder) Associated morphology anomalie du développement false Inferred relationship Some 2
Congenital cystic adenomatoid malformation of lung (disorder) Finding site Lung structure false Inferred relationship Some 2
Congenital cystic adenomatoid malformation of lung (disorder) Occurrence Congenital false Inferred relationship Some 3
Congenital cystic adenomatoid malformation of lung (disorder) Finding site Lung structure false Inferred relationship Some 3
Congenital cystic adenomatoid malformation of lung (disorder) Associated morphology Congenital cavitation false Inferred relationship Some 3
Congenital cystic adenomatoid malformation of lung (disorder) Occurrence Congenital true Inferred relationship Some 1
Congenital cystic adenomatoid malformation of lung (disorder) Pathological process (attribute) Pathological developmental process true Inferred relationship Some 1
Congenital cystic adenomatoid malformation of lung (disorder) Is a Congenital anomaly of lung true Inferred relationship Some
Congenital cystic adenomatoid malformation of lung (disorder) Associated morphology Cystic dilatation true Inferred relationship Some 1
Congenital cystic adenomatoid malformation of lung (disorder) Is a Lesion of lung true Inferred relationship Some

Inbound Relationships Type Active Source Characteristic Refinability Group
Congenital pulmonary airway malformation type 4 originates in the acinar structures of the lung. It consists of peripheral thin-walled cysts, typically affecting a single lobe. There is a strong association with type 1 pleuropulmonary blastoma. Is a True Congenital cystic adenomatoid malformation of lung (disorder) Inferred relationship Some
Congenital pulmonary airway malformation type 2 originates in the bronchiolar regions and is the second most frequent type, comprising 15-25% of cases. It may be associated with other types of renal or cardiac anomalies. Usually, it presents as multiple small cysts less than 2cm in diameter. The prognosis is good with no malignant potential. Is a True Congenital cystic adenomatoid malformation of lung (disorder) Inferred relationship Some
Congenital pulmonary airway malformation type 3 originates in the bronchiolar regions and may involve an entire lobe, compressing other lobes. It comprises 10% of all cases and the lesions may be solid not cystic and are less than 5mm in diameter. The prognosis is good with no malignant potential; however, there is typically an absence of pulmonary arteries within the lesion. Is a True Congenital cystic adenomatoid malformation of lung (disorder) Inferred relationship Some
Congenital pulmonary airway malformation type 1 is the commonest type, comprising about 70% of all cases. The cysts in this type are usually located within a single lobe and lined with columnar epithelium. There are often 1 or 2 large cysts up to 10cm in size which may be surrounded by smaller cysts. Is a True Congenital cystic adenomatoid malformation of lung (disorder) Inferred relationship Some
Congenital pulmonary airway malformation type 0 originates in the trachea or bronchi with acinar dysgenesis, cartilage, smooth muscles, and glands separated by mesenchyme. It is fatal after birth. Is a True Congenital cystic adenomatoid malformation of lung (disorder) Inferred relationship Some

This concept is not in any reference sets

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