1153417000: Secondary hemophagocytic lymphohistiocytosis (disorder)

SNOMED CT Concept\Clinical finding (finding)\...

\Finding of blood, lymphatics and immune system\Disorder of cellular component of blood (disorder)\White blood cell disorder\Qualitative abnormality of granulocyte\Combined phagocytic defect\Haemophagocytic lymphohistiocytosis\Secondary hemophagocytic lymphohistiocytosis (disorder)

\Disease\Disorder of immune function (disorder)\Immunodeficiency disorder\Primary immune deficiency disorder\Phagocytic cell defect\Phagocytic cell dysfunction (disorder)\Combined phagocytic defect\Haemophagocytic lymphohistiocytosis\Secondary hemophagocytic lymphohistiocytosis (disorder)
\Disease\Disorder of immune function (disorder)\White blood cell disorder\Qualitative abnormality of granulocyte\Combined phagocytic defect\Haemophagocytic lymphohistiocytosis\Secondary hemophagocytic lymphohistiocytosis (disorder)
\Disease\Disorder of hematopoietic cell proliferation (disorder)\Histiocytic syndrome\Haemophagocytic lymphohistiocytosis\Secondary hemophagocytic lymphohistiocytosis (disorder)
\Disease\Disorder of cellular component of blood (disorder)\White blood cell disorder\Qualitative abnormality of granulocyte\Combined phagocytic defect\Haemophagocytic lymphohistiocytosis\Secondary hemophagocytic lymphohistiocytosis (disorder)
\Disease\Disorder of body system\Disorder of immune structure (disorder)\Combined phagocytic defect\Haemophagocytic lymphohistiocytosis\Secondary hemophagocytic lymphohistiocytosis (disorder)
\Disease\Disorder of body system\Disorder of hematopoietic structure (disorder)\Haemophagocytic lymphohistiocytosis\Secondary hemophagocytic lymphohistiocytosis (disorder)

Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2021. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module

4564259011 Secondary hemophagocytic lymphohistiocytosis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core

4564260018 Secondary hemophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core

4564261019 Secondary haemophagocytic lymphohistiocytosis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core

7710811000241114 lymphohistiocytose hémophagocytaire secondaire fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module

Expanded Value Set

Outbound Relationships	Type	Target	Active	Characteristic	Refinability	Group	Values
Secondary hemophagocytic lymphohistiocytosis (disorder)	Due to	Disease	true	Inferred relationship	Some	1
Secondary hemophagocytic lymphohistiocytosis (disorder)	Is a	Haemophagocytic lymphohistiocytosis	true	Inferred relationship	Some
Secondary hemophagocytic lymphohistiocytosis (disorder)	Associated morphology	Histiocytic proliferation - category	false	Inferred relationship	Some	2
Secondary hemophagocytic lymphohistiocytosis (disorder)	Pathological process (attribute)	Abnormal immune process (qualifier value)	true	Inferred relationship	Some	2
Secondary hemophagocytic lymphohistiocytosis (disorder)	Finding site	Mononuclear phagocyte system structure (body structure)	true	Inferred relationship	Some	2
Secondary hemophagocytic lymphohistiocytosis (disorder)	Occurrence	Any period of life commencing after birth, but before death.	true	Inferred relationship	Some	2
Secondary hemophagocytic lymphohistiocytosis (disorder)	Associated morphology	Histiocytic proliferation (morphologic abnormality)	true	Inferred relationship	Some	2

Inbound Relationships	Type	Active	Source	Characteristic	Refinability	Group
A rare, secondary hemophagocytic lymphohistiocytosis characterized by occurring as either initial presentation of a malignant disease or at any stage during chemotherapy. The common associated malignancies are leukemias, B-cell, T-cell or NK-cell lymphomas, and Hodgkin lymphoma. Typical clinical manifestation includes fever, hepatosplenomegaly and cytopenias, combined with specific laboratory findings.	Is a	True	Secondary hemophagocytic lymphohistiocytosis (disorder)	Inferred relationship	Some
Hemophagocytic lymphohistiocytosis due to infection (disorder)	Is a	True	Secondary hemophagocytic lymphohistiocytosis (disorder)	Inferred relationship	Some

This concept is not in any reference sets