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1156631003: Dendritic cell sarcoma (morphologic abnormality)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2021. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
4575470010 Dendritic cell sarcoma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
4575471014 Dendritic cell sarcoma (morphologic abnormality) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Dendritic cell sarcoma Is a Dendritic cell neoplasm (morphologic abnormality) true Inferred relationship Some
Dendritic cell sarcoma Is a Malignant neoplasm, primary false Inferred relationship Some
Dendritic cell sarcoma Is a Malignant histiocytic neoplasm - category false Inferred relationship Some
Dendritic cell sarcoma Is a Sarcoma - category false Inferred relationship Some
Dendritic cell sarcoma Is a Malignant histiocytic neoplasm (morphologic abnormality) true Inferred relationship Some
Dendritic cell sarcoma Is a Sarcoma (morphologic abnormality) true Inferred relationship Some

Inbound Relationships Type Active Source Characteristic Refinability Group
A rare dendritic cell tumour characterised by a neoplasm composed of spindled to ovoid cells with phenotypic features similar to those of normal indeterminate cells. The tumour cells consistently express S100 protein and CD1a, while langerin, specific B- and T-cell markers, CD30, the histiocytic marker CD163, and the follicular dendritic cell markers CD21, CD23, and CD35 are negative. Birbeck granules are absent on ultrastructural examination. Patients typically present with multiple papules, nodules, or plaques of the skin. Primary lymph node or splenic involvement is less common. Systemic symptoms are usually absent. The clinical course is highly variable. Associated morphology True Dendritic cell sarcoma Inferred relationship Some 1

This concept is not in any reference sets

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