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127070008: Malignant histiocytic disorder (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2005. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
358015 Malignant histiocytic disorder en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
731112015 Malignant histiocytic disorder (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
6340461000241117 affection histiocytaire maligne fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


35 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Malignant histiocytic disorder Is a Histiocytic syndrome false Inferred relationship Some
Malignant histiocytic disorder Is a Hematologic malignancy false Inferred relationship Some
Malignant histiocytic disorder Is a Disorder of lymphoid system (disorder) false Inferred relationship Some
Malignant histiocytic disorder Finding site Hematopoietic system structure false Inferred relationship Some
Malignant histiocytic disorder Finding site Leukocyte false Inferred relationship Some
Malignant histiocytic disorder Pathological process Malignant neoplastic process false Inferred relationship Some
Malignant histiocytic disorder Finding site Lymphoid system consists of lymph nodes, lymphatic vessels and organs that contain lymphoid tissue, e.g. thymus, spleen. false Inferred relationship Some 1
Malignant histiocytic disorder Associated morphology néoplasie maligne (morphologie) false Inferred relationship Some 1
Malignant histiocytic disorder Is a Malignant white blood cell disorder false Inferred relationship Some
Malignant histiocytic disorder Finding site Hematopoietic system structure false Inferred relationship Some 1
Malignant histiocytic disorder Associated morphology White blood cell abnormality false Inferred relationship Some
Malignant histiocytic disorder Is a Malignant neoplasm of lymphoid, hematopoietic and/or related tissue (disorder) true Inferred relationship Some
Malignant histiocytic disorder Associated morphology Malignant histiocytic neoplasm - category false Inferred relationship Some 1
Malignant histiocytic disorder Is a Histiocytic neoplasm (disorder) true Inferred relationship Some
Malignant histiocytic disorder Associated morphology Malignant histiocytic neoplasm (morphologic abnormality) true Inferred relationship Some 1

Inbound Relationships Type Active Source Characteristic Refinability Group
Histiocytic sarcoma (clinical) Is a True Malignant histiocytic disorder Inferred relationship Some
Malignant histiocytosis (disorder) Is a True Malignant histiocytic disorder Inferred relationship Some
Langerhans cell histiocytosis, disseminated (disorder) Is a True Malignant histiocytic disorder Inferred relationship Some
Acute monocytic leukemia, FAB M5 Is a False Malignant histiocytic disorder Inferred relationship Some
leucémie monocytaire/monoblastique aigue Is a False Malignant histiocytic disorder Inferred relationship Some
Interdigitating dendritic cell sarcoma (disorder) Is a True Malignant histiocytic disorder Inferred relationship Some
Fibroblastic reticular cell neoplasm (disorder) Is a True Malignant histiocytic disorder Inferred relationship Some
Langerhans cell sarcoma (disorder) Is a True Malignant histiocytic disorder Inferred relationship Some
Primary follicular dendritic cell sarcoma (disorder) Is a True Malignant histiocytic disorder Inferred relationship Some
Monocytic leukaemia Is a False Malignant histiocytic disorder Inferred relationship Some
Localized malignant reticulohistiocytoma Is a True Malignant histiocytic disorder Inferred relationship Some
Indeterminate dendritic cell neoplasm (disorder) Is a True Malignant histiocytic disorder Inferred relationship Some
A rare dendritic cell tumour characterised by a neoplasm composed of spindled to ovoid cells with phenotypic features similar to those of normal indeterminate cells. The tumour cells consistently express S100 protein and CD1a, while langerin, specific B- and T-cell markers, CD30, the histiocytic marker CD163, and the follicular dendritic cell markers CD21, CD23, and CD35 are negative. Birbeck granules are absent on ultrastructural examination. Patients typically present with multiple papules, nodules, or plaques of the skin. Primary lymph node or splenic involvement is less common. Systemic symptoms are usually absent. The clinical course is highly variable. Is a True Malignant histiocytic disorder Inferred relationship Some
Erdheim-Chester disease Is a True Malignant histiocytic disorder Inferred relationship Some
Blastic plasmacytoid dendritic cell neoplasm Is a True Malignant histiocytic disorder Inferred relationship Some

This concept is not in any reference sets

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