Inbound Relationships |
Type |
Active |
Source |
Characteristic |
Refinability |
Group |
Histiocytic sarcoma (clinical) |
Is a |
True |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
Malignant histiocytosis (disorder) |
Is a |
True |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
Langerhans cell histiocytosis, disseminated (disorder) |
Is a |
True |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
Acute monocytic leukemia, FAB M5 |
Is a |
False |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
leucémie monocytaire/monoblastique aigue |
Is a |
False |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
Interdigitating dendritic cell sarcoma (disorder) |
Is a |
True |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
Fibroblastic reticular cell neoplasm (disorder) |
Is a |
True |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
Langerhans cell sarcoma (disorder) |
Is a |
True |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
Primary follicular dendritic cell sarcoma (disorder) |
Is a |
True |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
Monocytic leukaemia |
Is a |
False |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
Localized malignant reticulohistiocytoma |
Is a |
True |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
Indeterminate dendritic cell neoplasm (disorder) |
Is a |
True |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
A rare dendritic cell tumour characterised by a neoplasm composed of spindled to ovoid cells with phenotypic features similar to those of normal indeterminate cells. The tumour cells consistently express S100 protein and CD1a, while langerin, specific B- and T-cell markers, CD30, the histiocytic marker CD163, and the follicular dendritic cell markers CD21, CD23, and CD35 are negative. Birbeck granules are absent on ultrastructural examination. Patients typically present with multiple papules, nodules, or plaques of the skin. Primary lymph node or splenic involvement is less common. Systemic symptoms are usually absent. The clinical course is highly variable. |
Is a |
True |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
Erdheim-Chester disease |
Is a |
True |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|
Blastic plasmacytoid dendritic cell neoplasm |
Is a |
True |
Malignant histiocytic disorder |
Inferred relationship |
Some |
|