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253528005: Arrhythmogenic right ventricular dysplasia (disorder)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2002. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
2609630015 Arrhythmogenic right ventricular dysplasia (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
2616057013 Arrhythmogenic right ventricular dysplasia en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3006642015 Arrhythmogenic right ventricular cardiomyopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
5074791000241114 dysplasie ventriculaire droite arythmogène fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
3450291001000118 Arrhythmogene rechtsventrikuläre Kardiomyopathie de Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


2 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Arrhythmogenic right ventricular dysplasia (disorder) Is a Right ventricular abnormality true Inferred relationship Some
Arrhythmogenic right ventricular dysplasia (disorder) Associated morphology anomalie congénitale false Inferred relationship Some 1
Arrhythmogenic right ventricular dysplasia (disorder) Finding site Structure of cardiovascular system subdivision (body structure) false Inferred relationship Some 2
Arrhythmogenic right ventricular dysplasia (disorder) Occurrence Congenital false Inferred relationship Some
Arrhythmogenic right ventricular dysplasia (disorder) Finding site Right cardiac ventricular structure (body structure) false Inferred relationship Some 1
Arrhythmogenic right ventricular dysplasia (disorder) Finding site Structure of cardiovascular system (body structure) false Inferred relationship Some 2
Arrhythmogenic right ventricular dysplasia (disorder) Is a Congenital heart disease false Inferred relationship Some
Arrhythmogenic right ventricular dysplasia (disorder) Is a Congenital anomaly of trunk false Inferred relationship Some
Arrhythmogenic right ventricular dysplasia (disorder) Is a Congenital anomaly of cardiovascular system false Inferred relationship Some
Arrhythmogenic right ventricular dysplasia (disorder) Associated morphology anomalie congénitale false Inferred relationship Some 1
Arrhythmogenic right ventricular dysplasia (disorder) Finding site Right cardiac ventricular structure (body structure) false Inferred relationship Some 1
Arrhythmogenic right ventricular dysplasia (disorder) Occurrence Congenital false Inferred relationship Some 2
Arrhythmogenic right ventricular dysplasia (disorder) Associated morphology anomalie du développement false Inferred relationship Some 2
Arrhythmogenic right ventricular dysplasia (disorder) Is a Cardiovascular system hereditary disorder true Inferred relationship Some
Arrhythmogenic right ventricular dysplasia (disorder) Finding site Right cardiac ventricular structure (body structure) false Inferred relationship Some 2
Arrhythmogenic right ventricular dysplasia (disorder) Occurrence Congenital false Inferred relationship Some 1
Arrhythmogenic right ventricular dysplasia (disorder) Is a Congenital anomaly of cardiac chamber (disorder) false Inferred relationship Some
Arrhythmogenic right ventricular dysplasia (disorder) Pathological process (attribute) Pathological developmental process false Inferred relationship Some 1
Arrhythmogenic right ventricular dysplasia (disorder) Associated morphology Morphologically abnormal structure true Inferred relationship Some 1
Arrhythmogenic right ventricular dysplasia (disorder) Is a Congenital abnormality of cardiac ventricle false Inferred relationship Some
Arrhythmogenic right ventricular dysplasia (disorder) Is a Cardiomyopathy true Inferred relationship Some
Arrhythmogenic right ventricular dysplasia (disorder) Is a Autosomal hereditary disorder true Inferred relationship Some
Arrhythmogenic right ventricular dysplasia (disorder) Finding site Structure of myocardium of right ventricle true Inferred relationship Some 1
Arrhythmogenic right ventricular dysplasia (disorder) Is a A disorder that affects the myocardial ion channels, altering the electrical properties of the heart and changing the ECG and/or predisposing the subject to pro-arrhythmic events. true Inferred relationship Some
Arrhythmogenic right ventricular dysplasia (disorder) Finding site Cardiac conducting system structure true Inferred relationship Some 2

Inbound Relationships Type Active Source Characteristic Refinability Group
A rare arrhythmogenic right ventricular cardiomyopathy (ARVC) and a cutaneous phenotype, characterized by peculiar wooly hair and palmoplantar keratoderma. Is a True Arrhythmogenic right ventricular dysplasia (disorder) Inferred relationship Some
Familial isolated arrhythmogenic right ventricular dysplasia (ARVC) is the familial autosomal dominant form of ARVC, a heart muscle disease characterized by life-threatening ventricular arrhythmias with left bundle branch block configuration that may manifest with palpitations, ventricular tachycardia, syncope and sudden fatal attacks, and that is due to dystrophy and fibro-fatty replacement of the right ventricular myocardium that may lead to right ventricular aneurysms. Is a True Arrhythmogenic right ventricular dysplasia (disorder) Inferred relationship Some

This concept is not in any reference sets

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