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397349003: Nodal marginal zone B-cell lymphoma (morphologic abnormality)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2003. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
1765267017 Nodal marginal zone B-cell lymphoma (morphologic abnormality) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
1777016011 Nodal marginal zone B-cell lymphoma en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core


1 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Nodal marginal zone B-cell lymphoma (morphologic abnormality) Is a Marginal zone B-cell lymphoma true Inferred relationship Some
Nodal marginal zone B-cell lymphoma (morphologic abnormality) Is a Mature (peripheral) B-cell neoplasm (morphologic abnormality) true Inferred relationship Some

Inbound Relationships Type Active Source Characteristic Refinability Group
Nodal marginal zone B-cell lymphoma is a rare, indolent B-cell non-Hodgkin lymphoma, characterized by abnormal clonal proliferation of mature B-lymphocytes with involvement of the lymph nodes, sometimes the bone marrow, and rarely the blood. Clinically it presents with disseminated peripheral, abdominal and/or thoracic lymphadenopathy. Cytopenia and bulky tumors (greater than 5 cm) are rare. Association with Hepatitis C virus and chronic inflammation has been reported. Associated morphology True Nodal marginal zone B-cell lymphoma (morphologic abnormality) Inferred relationship Some 1
Pediatric nodal marginal zone lymphoma (morphologic abnormality) Is a True Nodal marginal zone B-cell lymphoma (morphologic abnormality) Inferred relationship Some

Reference Sets

Description inactivation indicator reference set

GB English

US English

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