Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2020. Module: SNOMED CT core
Descriptions:
Id | Description | Lang | Type | Status | Case? | Module |
1771472017 | Lymphangiomatosis (disorder) | en | Fully specified name | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
1782571017 | Lymphangiomatosis | en | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT core |
5263741000241117 | lymphangiomatose | fr | Synonym (core metadata concept) | Active | Entire term case insensitive (core metadata concept) | SNOMED CT Switzerland NRC maintained Module |
Inbound Relationships | Type | Active | Source | Characteristic | Refinability | Group |
Segmental lymphangiomatosis (disorder) | Is a | False | Lymphangiomatosis (disorder) | Inferred relationship | Some | |
Systemic lymphangiomatosis | Is a | False | Lymphangiomatosis (disorder) | Inferred relationship | Some | |
Diffuse pulmonary lymphangiomatosis (disorder) | Is a | True | Lymphangiomatosis (disorder) | Inferred relationship | Some | |
A rare vascular anomaly or angioma characterized by multifocal malformed lymphatic channels lined by clusters or sheets of spindled lymphatic endothelial cells with a predilection for the thoracic cavity, but also involving extra-thoracic locations, especially bones and spleen. Typical clinical signs and symptoms are pericardial and pleural effusions, cough, dyspnea, bleeding, and fractures secondary to bone involvement. Prognosis is generally poor due to the progressive nature of the condition. | Is a | True | Lymphangiomatosis (disorder) | Inferred relationship | Some |
This concept is not in any reference sets