Inbound Relationships |
Type |
Active |
Source |
Characteristic |
Refinability |
Group |
Histiocytic neoplasm (morphology) |
Is a |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
|
Histiocytosis |
Is a |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
|
anémie hémolytique auto-immune avec érythrophagocytose (Fc portion de l'auto-anticorps) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Haemophagocytic lymphohistiocytosis |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Juvenile xanthogranuloma of iris |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
3 |
Juvenile xanthogranuloma of skin (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
2 |
Histiocytic syndrome |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Hemophagocytic syndrome |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
|
Xanthogranuloma |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
[X]Other histiocytosis syndromes |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
|
Xanthoma disseminatum (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
2 |
Juvenile xanthogranuloma (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Multiple eruptive juvenile xanthogranuloma (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Non-Langerhans cell histiocytic dermatosis (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Cutaneous reticulohistiocytosis (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Solitary reticulohistiocytoma (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Diffuse normolipemic plane xanthomatosis (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Necrobiotic xanthogranuloma (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Necrobiotic xanthogranuloma with paraproteinemia (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Malakoplakia (involving skin) (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
|
Undetermined cell histiocytosis (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Macrophage activation syndrome (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
3 |
Erdheim-Chester disease |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
|
Xanthogranuloma of choroid plexus |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Erdheim-Chester disease (morphologic abnormality) |
Is a |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
|
Chronic histiocytosis |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
2 |
A rare cutaneous disease and a systemic inherited histiocytosis mainly characterised by hyperpigmentation, hypertrichosis, hepatosplenomegaly, heart anomalies, hearing loss, hypogonadism, low height, and occasionally, hyperglycaemia/diabetes mellitus. Due to overlapping clinical features, it is now considered to include pigmented hypertrichosis with insulin dependent diabetes mellitus syndrome (PHID), Faisalabad histiocytosis (FHC) and familial sinus histiocytosis with massive lymphadenopathy (FSHML). Some cases of dysosteosclerosis may also represent the syndrome. |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Hemophagocytic syndrome with human immunodeficiency virus infection (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
3 |
Primary hemophagocytic lymphohistiocytosis |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
2 |
Dermal dendritic cell histiocytosis |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Papular xanthoma is a form of non-Langerhans cell histiocytosis characterized by cutaneous presentation of solitary or disseminated yellow to orange-brown papular or papulonodular, noncoalescent, asymptomatic skin lesions located predominantly on the head, neck, trunk and extremities (rarely on oral mucosa), in the presence of normolipidemia. Microscopically, the lesions consist of monomorphous infiltrate of xanthomatous macrophages and numerous Touton giant cells, with scant or absent inflammatory infiltrate. It is usually not associated with systemic disease. |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Progressive nodular histiocytosis is a rare, normolipemic, non-Langerhans cell histiocytosis characterized by progressive growth of multiple to disseminated, asymptomatic skin lesions that range in appearance from yellow plaques to coalescence-prone red-brown papules, nodules and pedunculated tumors up to 5 cm in size, located typically on the face, trunk and extremities (and rarely on conjunctiva and mucous membranes). Characteristic microscopic findings include a storiform spindle cell infiltrate in the deep dermis with xanthomatous macrophages and some Touton cells in the upper dermis. It is usually not associated with systemic disease. |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
A rare, secondary hemophagocytic lymphohistiocytosis characterized by occurring as either initial presentation of a malignant disease or at any stage during chemotherapy. The common associated malignancies are leukemias, B-cell, T-cell or NK-cell lymphomas, and Hodgkin lymphoma. Typical clinical manifestation includes fever, hepatosplenomegaly and cytopenias, combined with specific laboratory findings. |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Juvenile xanthogranuloma of iris |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Juvenile xanthogranuloma of skin (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Xanthogranuloma (morphologic abnormality) |
Is a |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
|
Familial hemophagocytic lymphohistiocytosis (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
2 |
Macrophage activation syndrome (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
2 |
Hemophagocytic syndrome with human immunodeficiency virus infection (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Hemophagocytic lymphohistiocytosis due to infection (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
3 |
Hemophagocytic lymphohistiocytosis due to malignant disease |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |
Secondary hemophagocytic lymphohistiocytosis (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
2 |
Solitary reticulohistiocytoma (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
2 |
Cutaneous reticulohistiocytosis (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
2 |
Macrophage activation syndrome due to juvenile systemic onset arthritis |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
3 |
Hemophagocytic lymphohistiocytosis due to infection (disorder) |
Associated morphology |
False |
Histiocytic proliferation - category |
Inferred relationship |
Some |
1 |