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427213005: Autoimmune vasculitis (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2007. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
2662170019 Autoimmune vasculitis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
2675978018 Autoimmune vasculitis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
1854841000195110 vasculite autoimmune it Synonym (core metadata concept) Active Entire term case sensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
224131000172112 vascularite auto-immune fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


40 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Autoimmune vasculitis (disorder) Is a Vasculitis (disorder) true Inferred relationship Some
Autoimmune vasculitis (disorder) Associated morphology inflammation false Inferred relationship Some 1
Autoimmune vasculitis (disorder) Pathological process (attribute) Autoimmune process false Inferred relationship Some 2
Autoimmune vasculitis (disorder) Finding site Blood vessel structure (body structure) false Inferred relationship Some 1
Autoimmune vasculitis (disorder) Associated morphology inflammation false Inferred relationship Some 1
Autoimmune vasculitis (disorder) Finding site Blood vessel structure (body structure) true Inferred relationship Some 1
Autoimmune vasculitis (disorder) Is a Autoimmune disease true Inferred relationship Some
Autoimmune vasculitis (disorder) Associated morphology Inflammatory morphology (morphologic abnormality) true Inferred relationship Some 1
Autoimmune vasculitis (disorder) Pathological process (attribute) Autoimmune process true Inferred relationship Some 1

Inbound Relationships Type Active Source Characteristic Refinability Group
Immunoglobulin A vasculitis Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
Systemic lupus erythematosus encephalitis Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
vascularite rhumatoïde Is a False Autoimmune vasculitis (disorder) Inferred relationship Some
Rheumatoid arteritis Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
Allergic granulomatosis angiitis (disorder) Is a False Autoimmune vasculitis (disorder) Inferred relationship Some
STING-associated vasculopathy with onset in infancy (disorder) Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
A rare inflammatory, necrotizing, systemic vasculitis that affects predominantly small vessels (i.e. small arteries, arterioles, capillaries, venules) in multiple organs, including the kidney, the lungs, the skin and the peripheral nerves. Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
Acute rheumatic fever with aortitis (disorder) Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
A rare systemic autoimmune disease characterized by infiltrates of IgG4-positive plasma cells and lymphocytes in the adventitia of the aorta, resulting in thickening of perivascular tissue or formation of soft tissue masses surrounding the aorta and its major branches (potentially complicated by inflammatory aortic aneurysm), associated with elevated serum IgG4 levels. Preferential location is the infra-renal portion of the abdominal aorta. In addition, medium-sized blood vessels can be involved, and the condition may occur together with IgG4-related disease in other parts of the body. Clinical symptoms are unspecific and include chest or back pain and fever. Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
Vasculitis due to ADA2 deficiency is a rare, genetic, systemic and rheumatologic disease due to adenosine deaminase-2 inactivating mutations, combining variable features of autoinflammation, vasculitis, and a mild immunodeficiency. Variable clinical presentation includes chronic or recurrent systemic inflammation with fever, livedo reticularis or racemosa, early-onset ischaemic or haemorrhagic strokes, peripheral neuropathy, abdominal pain, hepatosplenomegaly, portal hypertension, cutaneous polyarteritis nodosa, variable cytopenia and immunoglobulin deficiency. Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
Rheumatoid arthritis with systemic vasculitis (disorder) Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
Cogan's syndrome (disorder) Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
Behcet's syndrome Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
Essential mixed cryoglobulinaemia Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
Granulomatosis with polyangiitis Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
Rheumatoid arthritis with necrotizing vasculitis (disorder) Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
Rheumatoid arthritis with isolated nailfold vasculitis (disorder) Is a True Autoimmune vasculitis (disorder) Inferred relationship Some
Rheumatoid arthritis with nailfold and finger-pulp infarcts (disorder) Is a True Autoimmune vasculitis (disorder) Inferred relationship Some

This concept is not in any reference sets

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