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443899007: Autoimmune inflammation of skeletal muscle (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2010. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
2836972017 Autoimmune inflammation of skeletal muscle (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
2841163014 Autoimmune inflammation of skeletal muscle en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
2841164015 Autoimmune myositis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
452761000172112 inflammation auto-immune des muscles squelettiques fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


5 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Autoimmune inflammation of skeletal muscle (disorder) Is a Inflammation of skeletal muscle, not including inflammation of cardiac muscle true Inferred relationship Some
Autoimmune inflammation of skeletal muscle (disorder) Pathological process (attribute) Autoimmune process false Inferred relationship Some 2
Autoimmune inflammation of skeletal muscle (disorder) Associated morphology inflammation false Inferred relationship Some 1
Autoimmune inflammation of skeletal muscle (disorder) Finding site Skeletal muscle structure false Inferred relationship Some 1
Autoimmune inflammation of skeletal muscle (disorder) Finding site Skeletal muscle structure true Inferred relationship Some 1
Autoimmune inflammation of skeletal muscle (disorder) Associated morphology inflammation false Inferred relationship Some 1
Autoimmune inflammation of skeletal muscle (disorder) Is a Autoimmune disease true Inferred relationship Some
Autoimmune inflammation of skeletal muscle (disorder) Is a Inflammation of specific body organs false Inferred relationship Some
Autoimmune inflammation of skeletal muscle (disorder) Associated morphology Inflammatory morphology (morphologic abnormality) true Inferred relationship Some 1
Autoimmune inflammation of skeletal muscle (disorder) Pathological process (attribute) Autoimmune process true Inferred relationship Some 1

Inbound Relationships Type Active Source Characteristic Refinability Group
A rare acquired skeletal muscle disease characterized by infiltration of the epimysium, perimysium, and perifascicular endomysium by macrophages with crystal inclusions composed of aluminum salts at the site of a previous vaccination (most commonly the deltoid muscle). Muscle necrosis is typically absent. Patients may present with myalgias, arthralgias, muscle weakness, chronic fatigue, asthenia, fever, and cognitive dysfunction. Signs and symptoms usually develop slowly over several months. Is a True Autoimmune inflammation of skeletal muscle (disorder) Inferred relationship Some
A rare secondary neonatal autoimmune disease characterized by generalized weakness, severe hypotonia, absent or reduced deep tendon reflexes, and highly elevated serum creatine kinase levels presenting in the neonatal period. Perifascicular atrophy in the presence of a diffuse perivascular inflammatory cell exudate is observed on muscle biopsy. Is a True Autoimmune inflammation of skeletal muscle (disorder) Inferred relationship Some
A rare form of idiopathic inflammatory myopathy characterized by acute or subacute, severe, symmetrical, proximal muscle weakness usually associated with muscle-specific antibodies (anti-HMGCR or anti-SRP). Histopathological characteristics include myocyte necrosis and regeneration without significant inflammation, and C5b-9 deposition on non-necrotic myofibers. Is a True Autoimmune inflammation of skeletal muscle (disorder) Inferred relationship Some
A rare juvenile idiopathic inflammatory myopathy characterized by the association of inflammatory myositis (manifesting with acral erythema, progressive weakness of the limbs, pain, general fatigue, moodiness or crankiness) with clinical and/or laboratory features of other autoimmune diseases (e.g. systemic lupus erythematosus, localized scleroderma, diabetes). Cardiac involvement has been reported in some patients. Is a True Autoimmune inflammation of skeletal muscle (disorder) Inferred relationship Some
A rare idiopathic inflammatory myopathy (IIM) with a heterogeneous phenotype characterized by myositis with at least one clinical and/or autoantibody overlap feature. Possible clinical overlap features include polyarthritis, Raynaud's phenomenon, sclerodactyly, scleroderma (proximal to metacarpophalangeal joints), lung interstitial pneumonia, and/or clinical signs of systemic lupus erythematosus (SLE). Is a True Autoimmune inflammation of skeletal muscle (disorder) Inferred relationship Some

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