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450908002: Primary cutaneous gamma-delta T-cell lymphoma (morphologic abnormality)

Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2012. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
2920583018 Primary cutaneous gamma-delta T-cell lymphoma (morphologic abnormality) en Fully specified name Active Only initial character case insensitive (core metadata concept) SNOMED CT core
2920598016 Primary cutaneous gamma-delta T-cell lymphoma en Synonym (core metadata concept) Active Only initial character case insensitive (core metadata concept) SNOMED CT core

0 descendants.

Expanded Value Set

Outbound Relationships Type Target Active Characteristic Refinability Group Values
Primary cutaneous gamma-delta T-cell lymphoma (morphologic abnormality) Is a Primary cutaneous T-cell lymphoma - category false Inferred relationship Some
Primary cutaneous gamma-delta T-cell lymphoma (morphologic abnormality) Is a Primary cutaneous T-cell lymphoma (morphologic abnormality) true Inferred relationship Some
Inbound Relationships Type Active Source Characteristic Refinability Group
Primary cutaneous gamma/delta-positive T-cell lymphoma is a rare, usually aggressive, subtype of cutaneous T-cell lymphoma characterized by infiltration of the epidermis, dermis or subcutaneous tissue by a clonal population of mature, gamma/delta positive cytotoxic T-cells. Typically it presents with ulcerating plaques, tumors, or subcutaneous nodules on the skin of the extremities, however, frequent involvement of mucosal and extranodal sites (such as the nasal cavity, gastrointestinal tract or lungs) is also observed. Cases associated with panniculitis may present with hemophagocytic syndrome (abrupt onset of fever, rash, cytopenia, hepatosplenomegaly and neurological compromise). Infiltration of lymph nodes, spleen and bone marrow is uncommon and resistance to multilineage chemotherapy is reported. Associated morphology True Primary cutaneous gamma-delta T-cell lymphoma (morphologic abnormality) Inferred relationship Some 1

This concept is not in any reference sets

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