Inbound Relationships |
Type |
Active |
Source |
Characteristic |
Refinability |
Group |
Variant Creutzfeldt-Jakob disease (disorder) |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Scrapie |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Bovine spongiform encephalopathy |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Creutzfeldt-Jakob disease |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Spongy degeneration of central nervous system |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Kuru |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Spongiform encephalopathy |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Prion disease |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Chronic wasting disease of captive mule deer AND/OR elk |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Gerstmann-Straussler-Scheinker syndrome |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Transmissible mink encephalopathy |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Fatal familial insomnia |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Progressive subcortical gliosis |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
[X]Dementia in Creutzfeldt-Jakob disease |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
maladie à prion associée au SIDA |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
maladie à prion associée au SIDA |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Creutzfeldt-Jakob disease |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Fatal familial insomnia |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Spongy degeneration of central nervous system |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Spongiform encephalopathy |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Transmissible mink encephalopathy |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Prion disease |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
[X]Dementia in Creutzfeldt-Jakob disease |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Chronic wasting disease of captive mule deer AND/OR elk |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Progressive subcortical gliosis |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Variant Creutzfeldt-Jakob disease (disorder) |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Kuru |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Scrapie |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Bovine spongiform encephalopathy |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Gerstmann-Straussler-Scheinker syndrome |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Gerstmann-Straussler-Scheinker syndrome |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
3 |
Kuru |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
3 |
Gerstmann-Straussler-Scheinker syndrome |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
2 |
Creutzfeldt-Jakob disease |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
3 |
Prion disease |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
3 |
Spongiform encephalopathy |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
2 |
Kuru |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
2 |
Fatal familial insomnia |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
3 |
Variant Creutzfeldt-Jakob disease (disorder) |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
2 |
Progressive subcortical gliosis |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
3 |
Sporadic Creutzfeldt-Jakob disease (disorder) |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
2 |
Variant Creutzfeldt-Jakob disease (disorder) |
Associated morphology |
False |
Spongy degeneration |
Inferred relationship |
Some |
3 |
Iatrogenic Jakob-Creutzfeldt disease (disorder) |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Inherited or familial Creutzfeldt-Jakob disease (fCJD) is a very rare form of genetic prion disease characterized by typical CJD features (rapidly progressive dementia, personality/behavioral changes, psychiatric disorders, myoclonus, and ataxia) with a genetic cause and sometimes a family history of dementia. |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Familial Alzheimer-like prion disease is an exceedingly rare form of prion disease characterized by the neuropathological features of Alzheimer disease including memory impairment and depression, related to abnormal prion protein (PrP) caused by a gene mutation in PRNP. Patients present with a prolonged, atypical course (absence of myoclonus or ataxia) unlike other forms of prion disease with severe neurofibrillary tangle pathology and high levels of cerebral amyloidosis. |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Variably protease sensitive prionopathy (disorder) |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Acquired prion disease (disorder) |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
A rare, autosomal dominant neurological disorder due to truncation mutations of the prion protein gene PRNP (20p13) leading to deposition of prion protein amyloid. Onset is usually in the fourth decade of life and reported clinical manifestations include diarrhea, nausea, autonomic failure (areflexia, weakness), neurogenic bladder and urinary infections. |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
2 |
Classical sporadic Creutzfeldt-Jakob disease |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Creutzfeldt-Jakob Disease caused by human growth hormone |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Creutzfeldt-Jakob Disease caused by human growth hormone |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
2 |
Sporadic infantile bilateral striatal necrosis |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Creutzfeldt Jakob disease following graft of dura (disorder) |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Sporadic fatal insomnia |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |
Sporadic Creutzfeldt-Jakob disease (disorder) |
Associated morphology |
True |
Spongy degeneration |
Inferred relationship |
Some |
1 |