702380008: Idiopathic inflammatory myopathy (disorder)

SNOMED CT Concept\Clinical finding (finding)\...

\General finding of soft tissue\Disorder of soft tissue\Disorder of skeletal muscle\Inflammation of skeletal muscle, not including inflammation of cardiac muscle\Idiopathic inflammatory myopathy (disorder)

\Muscle finding\Disorder of muscle\Disorder of skeletal muscle\Inflammation of skeletal muscle, not including inflammation of cardiac muscle\Idiopathic inflammatory myopathy (disorder)

\Musculoskeletal finding\Disorder of musculoskeletal system (disorder)\...

\Inflammatory disorder of musculoskeletal system\Inflammation of skeletal muscle, not including inflammation of cardiac muscle\Idiopathic inflammatory myopathy (disorder)

\Disorder of skeletal muscle\Inflammation of skeletal muscle, not including inflammation of cardiac muscle\Idiopathic inflammatory myopathy (disorder)

\Disease\Disorder of body system\Inflammation of specific body systems\Inflammatory disorder of musculoskeletal system\Inflammation of skeletal muscle, not including inflammation of cardiac muscle\Idiopathic inflammatory myopathy (disorder)
\Disease\Disorder of body system\Disorder of musculoskeletal system (disorder)\Inflammatory disorder of musculoskeletal system\Inflammation of skeletal muscle, not including inflammation of cardiac muscle\Idiopathic inflammatory myopathy (disorder)
\Disease\Disorder of body system\Disorder of musculoskeletal system (disorder)\Disorder of skeletal muscle\Inflammation of skeletal muscle, not including inflammation of cardiac muscle\Idiopathic inflammatory myopathy (disorder)
\Disease\Disorder of muscle\Disorder of skeletal muscle\Inflammation of skeletal muscle, not including inflammation of cardiac muscle\Idiopathic inflammatory myopathy (disorder)
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body systems\Inflammatory disorder of musculoskeletal system\Inflammation of skeletal muscle, not including inflammation of cardiac muscle\Idiopathic inflammatory myopathy (disorder)
\Disease\Inflammatory disorder\Inflammation of specific body structures or tissue\Inflammation of specific body organs\Inflammation of skeletal muscle, not including inflammation of cardiac muscle\Idiopathic inflammatory myopathy (disorder)
\Disease\Idiopathic disease\Idiopathic inflammatory myopathy (disorder)
\Disease\Disorder of soft tissue\Disorder of skeletal muscle\Inflammation of skeletal muscle, not including inflammation of cardiac muscle\Idiopathic inflammatory myopathy (disorder)

Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2019. Module: SNOMED CT core

Descriptions:

Expanded Value Set

Outbound Relationships	Type	Target	Active	Characteristic	Refinability	Group	Values
Idiopathic inflammatory myopathy (disorder)	Is a	myopathie inflammatoire	false	Inferred relationship	Some
Idiopathic inflammatory myopathy (disorder)	Associated morphology	Inflammatory morphology (morphologic abnormality)	true	Inferred relationship	Some	1
Idiopathic inflammatory myopathy (disorder)	Finding site	Skeletal and/or smooth muscle structure (body structure)	false	Inferred relationship	Some	1
Idiopathic inflammatory myopathy (disorder)	Is a	Idiopathic disease	true	Inferred relationship	Some
Idiopathic inflammatory myopathy (disorder)	Is a	Inflammation of skeletal muscle, not including inflammation of cardiac muscle	true	Inferred relationship	Some
Idiopathic inflammatory myopathy (disorder)	Finding site	Skeletal muscle structure	true	Inferred relationship	Some	1

Inbound Relationships	Type	Active	Source	Characteristic	Refinability	Group
A rare form of idiopathic inflammatory myopathy characterized by acute or subacute, severe, symmetrical, proximal muscle weakness usually associated with muscle-specific antibodies (anti-HMGCR or anti-SRP). Histopathological characteristics include myocyte necrosis and regeneration without significant inflammation, and C5b-9 deposition on non-necrotic myofibers.	Is a	True	Idiopathic inflammatory myopathy (disorder)	Inferred relationship	Some
A rare juvenile idiopathic inflammatory myopathy characterized by the association of inflammatory myositis (manifesting with acral erythema, progressive weakness of the limbs, pain, general fatigue, moodiness or crankiness) with clinical and/or laboratory features of other autoimmune diseases (e.g. systemic lupus erythematosus, localized scleroderma, diabetes). Cardiac involvement has been reported in some patients.	Is a	True	Idiopathic inflammatory myopathy (disorder)	Inferred relationship	Some
A rare idiopathic inflammatory myopathy characterized by diffuse destructive infiltration of CD68+ macrophages into the fascia rather than muscle fibers in muscle biopsies, proximal muscle weakness and myalgia with or without scaly dermatomyositis-like or atypical non-dermatomyositis-like skin lesions, elevation of creatine kinase levels and thickening of muscle fascia in muscle MRI.	Is a	True	Idiopathic inflammatory myopathy (disorder)	Inferred relationship	Some
A rare idiopathic inflammatory myopathy characterized by eosinophilic infiltration and inflammatory lesions of the skeletal muscle tissue, in the absence of an identifiable causative factor (e.g. parasitic infection, drug intake, systemic or malignant disease). Clinically patients may present focal or generalized muscle weakness and pain, difficulties to walk, motor clumsiness and/or mild bilateral Achilles tendon contracture, as well as elevated serum creatine kinase levels and peripheral blood and/or bone marrow hypereosinophilia.	Is a	True	Idiopathic inflammatory myopathy (disorder)	Inferred relationship	Some
Idiopathic polymyositis	Is a	True	Idiopathic inflammatory myopathy (disorder)	Inferred relationship	Some
Idiopathic dermatomyositis	Is a	True	Idiopathic inflammatory myopathy (disorder)	Inferred relationship	Some
A rare idiopathic inflammatory myopathy (IIM) with a heterogeneous phenotype characterized by myositis with at least one clinical and/or autoantibody overlap feature. Possible clinical overlap features include polyarthritis, Raynaud's phenomenon, sclerodactyly, scleroderma (proximal to metacarpophalangeal joints), lung interstitial pneumonia, and/or clinical signs of systemic lupus erythematosus (SLE).	Is a	True	Idiopathic inflammatory myopathy (disorder)	Inferred relationship	Some

Reference Sets

Description inactivation indicator reference set

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US English

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Id	Description	Lang	Type	Status	Case?	Module
2995372019	Idiopathic inflammatory myopathy (disorder)	en	Fully specified name	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
2995410015	Idiopathic inflammatory myopathy	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
2995743017	Idiopathic inflammatory myositis	en	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT core
868971000172115	IMM - immune mediated myopathy	fr	Synonym (core metadata concept)	Active	Entire term case sensitive (core metadata concept)	SNOMED CT Switzerland NRC maintained Module
937571000172112	myopathie inflammatoire idiopathique	fr	Synonym (core metadata concept)	Active	Entire term case insensitive (core metadata concept)	SNOMED CT Switzerland NRC maintained Module