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721308005: Acute leukemia of ambiguous lineage (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2017. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
3324926017 Acute leukemia of ambiguous lineage (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
3324927014 Acute leukemia of ambiguous lineage en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
3324928016 Acute leukaemia of ambiguous lineage en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
924221000172115 leucémie aigüe de lignée ambigüe fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module
992241000172112 leucémie aigüe de lignée intermédiaire fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


1 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Acute leukemia of ambiguous lineage (disorder) Is a Acute leukemia true Inferred relationship Some
Acute leukemia of ambiguous lineage (disorder) Associated morphology Acute leukemia of ambiguous lineage (morphologic abnormality) true Inferred relationship Some 1
Acute leukemia of ambiguous lineage (disorder) Finding site Bone marrow structure true Inferred relationship Some 1

Inbound Relationships Type Active Source Characteristic Refinability Group
A rare acute leukemia of ambiguous lineage characterized by clonal proliferation of primitive hematopoietic cells, primarily in the bone marrow and blood, lacking lineage-specific markers and detectable genotypic alterations. The patients present with leukocytosis, anemia, variable platelet count and a variety of nonspecific symptoms related to ineffective hematopoesis (fatigue, bleeding and bruising, recurrent infections, bone pain) and/or extramedullary site involvement (lymphadenopathy, splenomegaly, hepatomegaly). Is a True Acute leukemia of ambiguous lineage (disorder) Inferred relationship Some

This concept is not in any reference sets

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