737223000: Dendritic cell neoplasm (disorder)

SNOMED CT Concept\Clinical finding (finding)\Disease\...

\Disorder of hematopoietic cell proliferation (disorder)\Histiocytic syndrome\Histiocytic neoplasm (disorder)\Dendritic cell neoplasm

\Neoplasm and/or hamartoma (disorder)\Neoplastic disease\Neoplasm of hematopoietic cell type (disorder)\Histiocytic neoplasm (disorder)\Dendritic cell neoplasm

Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2018. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module

3527202011 Dendritic cell neoplasm en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core

3527203018 Dendritic cell neoplasm (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core

5876301000241111 néoplasme à cellules dendritiques fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module

5876311000241113 tumeur à cellules dendritiques fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module

Expanded Value Set

Outbound Relationships	Type	Target	Active	Characteristic	Refinability	Group	Values
Dendritic cell neoplasm	Associated morphology	Dendritic cell neoplasm (morphologic abnormality)	true	Inferred relationship	Some	1
Dendritic cell neoplasm	Is a	Histiocytic neoplasm (disorder)	true	Inferred relationship	Some

Inbound Relationships	Type	Active	Source	Characteristic	Refinability	Group
Langerhans cell histiocytosis	Is a	True	Dendritic cell neoplasm	Inferred relationship	Some
Interdigitating dendritic cell sarcoma (disorder)	Is a	True	Dendritic cell neoplasm	Inferred relationship	Some
Langerhans cell sarcoma (disorder)	Is a	True	Dendritic cell neoplasm	Inferred relationship	Some
Primary follicular dendritic cell sarcoma (disorder)	Is a	True	Dendritic cell neoplasm	Inferred relationship	Some
Indeterminate dendritic cell neoplasm (disorder)	Is a	True	Dendritic cell neoplasm	Inferred relationship	Some
A rare dendritic cell tumour characterised by a neoplasm composed of spindled to ovoid cells with phenotypic features similar to those of normal indeterminate cells. The tumour cells consistently express S100 protein and CD1a, while langerin, specific B- and T-cell markers, CD30, the histiocytic marker CD163, and the follicular dendritic cell markers CD21, CD23, and CD35 are negative. Birbeck granules are absent on ultrastructural examination. Patients typically present with multiple papules, nodules, or plaques of the skin. Primary lymph node or splenic involvement is less common. Systemic symptoms are usually absent. The clinical course is highly variable.	Is a	True	Dendritic cell neoplasm	Inferred relationship	Some

Reference Sets