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803009: Paraganglioma (morphologic abnormality)


Status: current, Not sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jan 2002. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
2405017 Paraganglioma en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
821446019 Paraganglioma (morphologic abnormality) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core


0 descendants.

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Paraganglioma Is a Paraganglioma AND/OR glomus tumor true Inferred relationship Some
Paraganglioma Is a Neoplasm of uncertain behaviour true Inferred relationship Some

Inbound Relationships Type Active Source Characteristic Refinability Group
[M]Paraganglioma NOS Is a False Paraganglioma Inferred relationship Some
Gangliocytic paraganglioma Associated morphology False Paraganglioma Inferred relationship Some 1
Extra-adrenal paraganglioma Associated morphology False Paraganglioma Inferred relationship Some 1
Neoplasm of carotid body Associated morphology False Paraganglioma Inferred relationship Some 3
Neoplasm of glomus jugulare Associated morphology False Paraganglioma Inferred relationship Some 2
Neoplasm of coccygeal body Associated morphology False Paraganglioma Inferred relationship Some 2
Benign neoplasm of carotid body Associated morphology False Paraganglioma Inferred relationship Some 1
Neoplasm of uncertain behavior of glomus jugulare Associated morphology False Paraganglioma Inferred relationship Some 1
Neoplasm of uncertain behavior of coccygeal body Associated morphology False Paraganglioma Inferred relationship Some 1
néoplasme glomique du nerf vague Associated morphology False Paraganglioma Inferred relationship Some 1
Glomus tympanicum tumor Associated morphology False Paraganglioma Inferred relationship Some 1
Benign neoplasm of coccygeal body Associated morphology False Paraganglioma Inferred relationship Some 3
Neoplasm of uncertain behavior of coccygeal body Associated morphology False Paraganglioma Inferred relationship Some 2
Neoplasm of uncertain behavior of glomus jugulare Associated morphology False Paraganglioma Inferred relationship Some 2
Paraganglioma Associated morphology True Paraganglioma Inferred relationship Some 1
Gangliocytic paraganglioma Associated morphology True Paraganglioma Inferred relationship Some 1
A rare, hereditary, pheochromocytoma/paraganglioma tumor arising from neuroendocrine chromaffin cells of the adrenal medulla (pheochromocytoma) or from any paraganglia from the skull base to the pelvic floor (paraganglioma). Clinical manifestations are often linked to excess catecholamines production causing sustained or paroxysmal elevations in blood pressure, headache, episodic profuse sweating, palpitations, pallor and apprehension or anxiety. Hereditary pheochromocytoma/paraganglioma tumors tend to present at younger ages, to be multi-focal, bilateral, and recurrent, or to have multiple synchronous neoplasms. Associated morphology True Paraganglioma Inferred relationship Some 1
Carney-Stratakis syndrome is a recently described familial syndrome characterized by gastrointestinal stromal tumors (GIST) and paragangliomas, often at multiple sites. Associated morphology False Paraganglioma Inferred relationship Some 4
Carney-Stratakis syndrome is a recently described familial syndrome characterized by gastrointestinal stromal tumors (GIST) and paragangliomas, often at multiple sites. Associated morphology True Paraganglioma Inferred relationship Some 2
A rare neuroendocrine tumor arising from neural crest-derived paraganglion cells (most often in the para-aortic region at the level of renal hilum, organ of Zuckerkandl, thoracic paraspinal region, bladder, and carotid body) not associated with catecholamine secretion. These tumors are usually clinically silent and symptoms, if present, are nonspecific and depend on the location of the tumor. Association with certain hereditary cancer-predisposing syndromes, such as multiple endocrine neoplasia, neurofibromatosis type 1 or von Hippel Lindau syndrome, may be observed. Associated morphology True Paraganglioma Inferred relationship Some 1
A rare, isolated, non-familial pheochromocytoma/paraganglioma tumor arising from neuroendocrine chromaffin cells of the adrenal medulla (pheochromocytoma) or from extra-adrenal chromaffin tissue (paraganglioma). The majority of these tumors are benign and the presenting symptoms are typically caused by the increased catecholamine production of the tumor, including hypertension (often paroxysmal), tachycardia, anxiety and/or excessive sweating. Associated morphology True Paraganglioma Inferred relationship Some 1
A rare, endocrine disease characterized by early onset of polycythemia, and later occurring multiple paraganglioma. Clinical presentation includes hypertension, headaches, fatigue, nausea, anxiety, and high concentration of red blood cells, leading to increased risk of stroke and pulmonary thromboembolism. Associated morphology True Paraganglioma Inferred relationship Some 2

This concept is not in any reference sets

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