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95643007: Autoimmune encephalitis (disorder)


Status: current, Sufficiently defined by necessary conditions definition status (core metadata concept). Date: 31-Jul 2004. Module: SNOMED CT core

Descriptions:

Id Description Lang Type Status Case? Module
158440010 Autoimmune encephalitis en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
512232018 Autoimmune encephalopathy en Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT core
839840010 Autoimmune encephalitis (disorder) en Fully specified name Active Entire term case insensitive (core metadata concept) SNOMED CT core
272331000077114 encéphalite auto-immune fr Synonym (core metadata concept) Active Entire term case insensitive (core metadata concept) SNOMED CT Switzerland NRC maintained Module


10 descendants. Search Descendants:

Expanded Value Set


Outbound Relationships Type Target Active Characteristic Refinability Group Values
Autoimmune encephalitis Is a Encephalitis true Inferred relationship Some
Autoimmune encephalitis Is a Autoimmune disease true Inferred relationship Some
Autoimmune encephalitis Is a encéphalopathies toxiques et métaboliques acquises false Inferred relationship Some
Autoimmune encephalitis Finding site Brain structure false Inferred relationship Some 1
Autoimmune encephalitis Associated morphology inflammation false Inferred relationship Some 1
Autoimmune encephalitis Finding site Structure of immune system (body structure) false Inferred relationship Some
Autoimmune encephalitis Finding site Brain tissue structure false Inferred relationship Some 1
Autoimmune encephalitis Pathological process (attribute) Autoimmune process false Inferred relationship Some 2
Autoimmune encephalitis Has definitional manifestation Immune system finding false Inferred relationship Some
Autoimmune encephalitis Associated morphology inflammation false Inferred relationship Some 1
Autoimmune encephalitis Finding site Brain tissue structure true Inferred relationship Some 1
Autoimmune encephalitis Is a Inflammation of specific body organs false Inferred relationship Some
Autoimmune encephalitis Associated morphology Inflammatory morphology (morphologic abnormality) true Inferred relationship Some 1
Autoimmune encephalitis Pathological process (attribute) Autoimmune process true Inferred relationship Some 1

Inbound Relationships Type Active Source Characteristic Refinability Group
Allergic encephalitis Is a False Autoimmune encephalitis Inferred relationship Some
Acute hemorrhagic leukoencephalitis Is a False Autoimmune encephalitis Inferred relationship Some
Systemic lupus erythematosus encephalitis Is a True Autoimmune encephalitis Inferred relationship Some
Autoimmune hypophysitis Is a False Autoimmune encephalitis Inferred relationship Some
Acute disseminated encephalomyelitis Is a True Autoimmune encephalitis Inferred relationship Some
Limbic encephalitis with contactin-associated protein-like 2 antibodies (disorder) Is a False Autoimmune encephalitis Inferred relationship Some
Limbic encephalitis with leucine-rich glioma-inactivated 1 antibodies Is a False Autoimmune encephalitis Inferred relationship Some
A rare neurologic disorder characterized by a unique non-REM and REM parasomnia with sleep breathing dysfunction, gait instability and repetitive episodes of respiratory insufficiency, as well as autoantibodies against IgLON5. Patients may present stridor, chorea, limb ataxia, abnormal ocular movements, and bulbar symptoms (i.e. dysphagia, dysarthria, episodic central hypoventilation) with normal brain MRI. Excessive day sleepiness and cognitive deterioration have also been reported. Is a True Autoimmune encephalitis Inferred relationship Some
Steroid-responsive encephalopathy associated with autoimmune thyroiditis (SREAT) is a rare, acquired, neurological disease characterized by encephalopathy associated with elevated antithyroid antibodies, in the absence of other causes. Clinical presentation varies from minor cognitive impairment to status epilepticus and coma, and frequently includes seizures, confusion, speech disorder, memory impairment, ataxia and psychiatric manifestations. Is a True Autoimmune encephalitis Inferred relationship Some
Limbic encephalitis with neurexin-3 antibodies (disorder) Is a False Autoimmune encephalitis Inferred relationship Some
Autoimmune acquired autonomic encephalomyelitis Is a True Autoimmune encephalitis Inferred relationship Some
Autoimmune encephalitis caused by N-methyl-D-aspartate receptor antibody (disorder) Is a True Autoimmune encephalitis Inferred relationship Some
Autoimmune inflammation of cerebellum (disorder) Is a False Autoimmune encephalitis Inferred relationship Some
Autonomic disorder due to autoimmune encephalitis Due to True Autoimmune encephalitis Inferred relationship Some 2
Dementia due to autoimmune encephalitis (disorder) Due to True Autoimmune encephalitis Inferred relationship Some 3
A rare autoimmune encephalitis involving the mesial temporal lobes and clinically characterised by subacute onset (rapid progression of less than three months) of short-term memory deficits, seizures or psychiatric symptoms, such as behavioural changes, anxiety, depression, and psychosis. Further diagnostic criteria are bilateral abnormalities restricted to the mesial temporal lobes in brain MRI, cerebrospinal fluid pleocytosis and/or epileptic or slow-wave activity involving the temporal lobes in EEG, and reasonable exclusion of alternative causes. Paraneoplastic or non-paraneoplastic antibodies against neuronal antigens may be found in serum and/or cerebrospinal fluid. Is a True Autoimmune encephalitis Inferred relationship Some
A rare autoimmune encephalitis characterized by various phenotypes depending on the region of the brainstem that is involved; patients present with gaze palsies (in midbrain involvement), facial palsy or vertical gaze palsies (in pontine involvement), dysarthria, dysphagia or central hypoventilation (in medullary involvement). Additional clinical features may also involve pyramidal symptoms and gait impairment. Is a True Autoimmune encephalitis Inferred relationship Some

Reference Sets

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